PRESENILE ONSET CEREBRAL ADRENOLEUKODYSTROPHY PRESENTING AS BALINTS-SYNDROME AND DEMENTIA

被引:15
作者
UYAMA, E
IWAGOE, H
MAEDA, J
NAKAMURA, M
TERASAKI, T
ANDO, M
机构
关键词
D O I
10.1212/WNL.43.6.1249
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We describe a patient with presenile-onset cerebral adrenoleukodystrophy presenting as Balint's syndrome and dementia. There were demyelinating MRI changes in the parieto-occipital white matter bilaterally, including the splenium of the corpus callosum. Therapeutic trials using 1-deamino-(8-D-arginine)-vasopressin, very long-chain fatty acid-free diet, and gamma-globulin were of no benefit.
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页码:1249 / 1251
页数:3
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