BIOENERGETIC HETEROGENEITY OF HUMAN MITOCHONDRIAL MYOPATHIES - PHOSPHORUS MAGNETIC-RESONANCE SPECTROSCOPY STUDY

被引:127
作者
ARGOV, Z
BANK, WJ
MARIS, J
PETERSON, P
CHANCE, B
机构
[1] HOSP UNIV PENN,DEPT NEUROL,PHILADELPHIA,PA 19104
[2] WAYNE STATE UNIV,CTR HLTH,DETROIT,MI 48202
关键词
D O I
10.1212/WNL.37.2.257
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:257 / 262
页数:6
相关论文
共 26 条
[1]  
ARGOV Z, 1985, ANN NEUROL, V18, P119
[2]   TREATMENT OF MITOCHONDRIAL MYOPATHY DUE TO COMPLEX-III DEFICIENCY WITH VITAMINS K3 AND C - A P-31-NMR FOLLOW-UP-STUDY [J].
ARGOV, Z ;
BANK, WJ ;
MARIS, J ;
ELEFF, S ;
KENNAWAY, NG ;
OLSON, RE ;
CHANCE, B .
ANNALS OF NEUROLOGY, 1986, 19 (06) :598-602
[3]  
ARGOV Z, 1985, ANN NEUROL, V18, P162
[4]   METABOLIC RECOVERY AFTER EXERCISE AND THE ASSESSMENT OF MITOCHONDRIAL-FUNCTION INVIVO IN HUMAN SKELETAL-MUSCLE BY MEANS OF P-31 NMR [J].
ARNOLD, DL ;
MATTHEWS, PM ;
RADDA, GK .
MAGNETIC RESONANCE IN MEDICINE, 1984, 1 (03) :307-315
[5]   INVESTIGATION OF HUMAN MITOCHONDRIAL MYOPATHIES BY PHOSPHORUS MAGNETIC-RESONANCE SPECTROSCOPY [J].
ARNOLD, DL ;
TAYLOR, DJ ;
RADDA, GK .
ANNALS OF NEUROLOGY, 1985, 18 (02) :189-196
[6]   APPLICATIONS OF P-31-NMR TO CLINICAL BIOCHEMISTRY [J].
CHANCE, B .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1984, 428 (JUN) :318-332
[7]  
CHANCE B, 1985, CIRCULATION, V72, P103
[8]   MITOCHONDRIAL REGULATION OF PHOSPHOCREATINE INORGANIC-PHOSPHATE RATIOS IN EXERCISING HUMAN-MUSCLE - A GATED P-31 NMR-STUDY [J].
CHANCE, B ;
ELEFF, S ;
LEIGH, JS ;
SOKOLOW, D ;
SAPEGA, A .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1981, 78 (11) :6714-6718
[9]   MITOCHONDRIAL MYOPATHIES [J].
DIMAURO, S ;
BONILLA, E ;
ZEVIANI, M ;
NAKAGAWA, M ;
DEVIVO, DC .
ANNALS OF NEUROLOGY, 1985, 17 (06) :521-538
[10]   P-31 NMR-STUDY OF IMPROVEMENT IN OXIDATIVE-PHOSPHORYLATION BY VITAMIN-K3 AND VITAMIN-C IN A PATIENT WITH A DEFECT IN ELECTRON-TRANSPORT AT COMPLEX-III IN SKELETAL-MUSCLE [J].
ELEFF, S ;
KENNAWAY, NG ;
BUIST, NRM ;
DARLEYUSMAR, VM ;
CAPALDI, RA ;
BANK, WJ ;
CHANCE, B .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1984, 81 (11) :3529-3533