ABNORMAL COMPACT MYELIN IN THE MYELIN-DEFICIENT RAT - ABSENCE OF PROTEOLIPID PROTEIN CORRELATES WITH A DEFECT IN THE INTRAPERIOD LINE

被引:123
作者
DUNCAN, ID [1 ]
HAMMANG, JP [1 ]
TRAPP, BD [1 ]
机构
[1] JOHNS HOPKINS UNIV,SCH MED,DEPT NEUROL,BALTIMORE,MD 21205
关键词
D O I
10.1073/pnas.84.17.6287
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:6287 / 6291
页数:5
相关论文
共 34 条
[1]  
CSIZA CK, 1979, AM J PATHOL, V95, P215
[2]  
CSIZA CK, 1982, J LIPID RES, V23, P720
[3]   THE STRUCTURAL GENE CODING FOR MYELIN-ASSOCIATED PROTEOLIPID PROTEIN IS MUTATED IN JIMPY MICE [J].
DAUTIGNY, A ;
MATTEI, MG ;
MORELLO, D ;
ALLIEL, PM ;
PHAMDINH, D ;
AMAR, L ;
ARNAUD, D ;
SIMON, D ;
MATTEI, JF ;
GUENET, JL ;
JOLLES, P ;
AVNER, P .
NATURE, 1986, 321 (6073) :867-869
[4]   GLIAL AND AXONAL DEVELOPMENT IN OPTIC-NERVE OF MYELIN DEFICIENT RAT MUTANT [J].
DENTINGER, MP ;
BARRON, KD ;
CSIZA, CK .
BRAIN RESEARCH, 1985, 344 (02) :255-266
[5]  
DENTINGER P, 1982, J NEUROCYTOL, V11, P671
[6]   INDIVIDUAL EXONS ENCODE THE INTEGRAL MEMBRANE DOMAINS OF HUMAN MYELIN PROTEOLIPID PROTEIN [J].
DIEHL, HJ ;
SCHAICH, M ;
BUDZINSKI, RM ;
STOFFEL, W .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1986, 83 (24) :9807-9811
[7]   SHAKING PUPS - A DISORDER OF CENTRAL MYELINATION IN THE SPANIEL DOG .2. ULTRASTRUCTURAL OBSERVATIONS ON THE WHITE MATTER OF THE CERVICAL SPINAL-CORD [J].
GRIFFITHS, IR ;
DUNCAN, ID ;
MCCULLOCH, M .
JOURNAL OF NEUROCYTOLOGY, 1981, 10 (05) :847-858
[8]   2',3'-CYCLIC NUCLEOTIDE 3'-PHOSPHODIESTERASE AND 5'-NUCLEOTIDASE IN THE CENTRAL NERVOUS-SYSTEM OF A MYELIN-DEFICIENT RAT MUTANT [J].
HOF, L ;
CSIZA, CK ;
DENTINGER, MP ;
BARRON, KD .
JOURNAL OF NEUROCHEMISTRY, 1984, 42 (06) :1767-1770
[9]   DEVELOPMENTAL-CHANGES IN GLYCOLIPID SYNTHESIZING ENZYMES IN THE BRAIN OF A MYELIN-DEFICIENT MUTANT WISTAR RAT [J].
HOF, L ;
CSIZA, CK .
JOURNAL OF NEUROCHEMISTRY, 1982, 39 (05) :1434-1439
[10]  
HUDSON L, 1985, J CELL BIOL, V101, P435