DETECTION OF EARLY ABNORMALITIES IN THE MUCOPOLYSACCHARIDOSES BY THE USE OF VISUAL AND BRAIN-STEM AUDITORY EVOKED-POTENTIALS

被引:4
作者
PERRETTI, A
PETRILLO, A
PELOSI, L
BALBI, P
PARENTI, G
RIEMMA, A
STRISCIUGLIO, P
机构
[1] NAPLES UNIV,SCH MED 2,DEPT PEDIAT,VIA S PANSINI 5,I-80131 NAPLES,ITALY
[2] NAPLES UNIV,SCH MED 2,DEPT CLIN NEUROPHYSIOL,I-80131 NAPLES,ITALY
关键词
brainstem auditory evoked potentials; flash visual evoked potentials; mucopolysaccharidoses;
D O I
10.1055/s-2008-1071467
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Flash visual evoked potentials (FVEPs) and brainstem auditory evoked potentials (BAEPs) were performed in 13 children (aged 3-17 years) affected by mucopolysaccharidoses (MPSs). FVEPs and BAEPs were abnormal in 6 and 9 patients, respectively. The presence of these abnormalities in most neurologically normal patients suggests that electrophysiological techniques provide a useful tool for detecting early abnormalities
引用
收藏
页码:83 / 86
页数:4
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