DETECTION OF EARLY ABNORMALITIES IN THE MUCOPOLYSACCHARIDOSES BY THE USE OF VISUAL AND BRAIN-STEM AUDITORY EVOKED-POTENTIALS

被引:4
|
作者
PERRETTI, A
PETRILLO, A
PELOSI, L
BALBI, P
PARENTI, G
RIEMMA, A
STRISCIUGLIO, P
机构
[1] NAPLES UNIV,SCH MED 2,DEPT PEDIAT,VIA S PANSINI 5,I-80131 NAPLES,ITALY
[2] NAPLES UNIV,SCH MED 2,DEPT CLIN NEUROPHYSIOL,I-80131 NAPLES,ITALY
关键词
brainstem auditory evoked potentials; flash visual evoked potentials; mucopolysaccharidoses;
D O I
10.1055/s-2008-1071467
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Flash visual evoked potentials (FVEPs) and brainstem auditory evoked potentials (BAEPs) were performed in 13 children (aged 3-17 years) affected by mucopolysaccharidoses (MPSs). FVEPs and BAEPs were abnormal in 6 and 9 patients, respectively. The presence of these abnormalities in most neurologically normal patients suggests that electrophysiological techniques provide a useful tool for detecting early abnormalities
引用
收藏
页码:83 / 86
页数:4
相关论文
共 50 条
  • [1] VISUAL EVOKED-POTENTIALS AND BRAIN-STEM AUDITORY EVOKED-POTENTIALS IN MIGRAINE
    BENNA, P
    BIANCO, C
    COSTA, P
    PIAZZA, D
    BERGAMASCO, B
    ELECTROENCEPHALOGRAPHY AND CLINICAL NEUROPHYSIOLOGY, 1987, 66 (03): : P54 - P54
  • [2] EARLY DETECTION OF BRAIN-STEM GLIOMA USING BRAIN-STEM AUDITORY EVOKED-POTENTIALS
    GUTHKELCH, AN
    VRIES, JK
    SCLABASSI, RJ
    DEVELOPMENTAL MEDICINE AND CHILD NEUROLOGY, 1985, 27 (03): : 331 - 334
  • [3] VISUAL EVOKED AND BRAIN-STEM AUDITORY EVOKED-POTENTIALS IN DIVERS
    TODNEM, K
    VAERNES, R
    KAMBESTAD, BK
    AVIATION SPACE AND ENVIRONMENTAL MEDICINE, 1991, 62 (10): : 982 - 985
  • [4] SOMATOSENSORY, VISUAL AND BRAIN-STEM AUDITORY EVOKED-POTENTIALS
    COSI, V
    CURRENT OPINION IN NEUROLOGY AND NEUROSURGERY, 1991, 4 (05): : 760 - 769
  • [5] BRAIN-STEM AUDITORY EVOKED-POTENTIALS
    RODER, H
    RABENDING, G
    KALLWELLIS, G
    ELECTROENCEPHALOGRAPHY AND CLINICAL NEUROPHYSIOLOGY, 1980, 50 (3-4): : P98 - P98
  • [6] ABNORMALITIES OF SOMATOSENSORY, VISUAL, AND BRAIN-STEM AUDITORY EVOKED-POTENTIALS IN AMYOTROPHIC LATERAL SCLEROSIS
    MATHESON, JK
    HARRINGTON, H
    HALLETT, M
    MUSCLE & NERVE, 1983, 6 (07) : 529 - 529
  • [7] ABNORMALITIES OF SOMATOSENSORY, VISUAL AND BRAIN-STEM AUDITORY EVOKED-POTENTIALS IN AMYOTROPHIC LATERAL SCLEROSIS
    MATHESON, JK
    HARRINGTON, H
    HALLETT, M
    ELECTROENCEPHALOGRAPHY AND CLINICAL NEUROPHYSIOLOGY, 1984, 57 (05): : P82 - P82
  • [8] BRAIN-STEM AUDITORY, VISUAL AND SOMATOSENSORY EVOKED-POTENTIALS IN LEUKODYSTROPHIES
    MARKAND, ON
    GARG, BP
    DEMYER, WE
    WARREN, C
    WORTH, RM
    ELECTROENCEPHALOGRAPHY AND CLINICAL NEUROPHYSIOLOGY, 1982, 54 (01): : 39 - 48
  • [9] VISUAL AND AUDITORY BRAIN-STEM EVOKED-POTENTIALS IN COMATOSE PATIENTS
    KONDAS, M
    BARTKO, D
    JANCO, S
    ELECTROENCEPHALOGRAPHY AND CLINICAL NEUROPHYSIOLOGY, 1985, 61 (01): : P11 - P11
  • [10] EARLY ABNORMALITIES OF BRAIN-STEM AUDITORY EVOKED-POTENTIALS IN FRIEDREICHS ATAXIA - EVIDENCE OF PRIMARY BRAIN-STEM DYSFUNCTION
    JABBARI, B
    SCHWARTZ, DM
    MACNEIL, DM
    COKER, SB
    NEUROLOGY, 1983, 33 (08) : 1071 - 1074