DYSTROPHIN-GLYCOPROTEIN COMPLEX - MOLECULAR-ORGANIZATION AND CRITICAL ROLES IN SKELETAL-MUSCLE

被引:67
作者
SUNADA, Y
CAMPBELL, KP
机构
[1] Howard Hughes Medical Institute, Department Physiology and Biophysics, University Iowa College of Medicine, Iowa City, IA 53243
关键词
D O I
10.1097/00019052-199510000-00010
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Recent molecular and biochemical studies have disclosed the detailed molecular organization of the dystrophin-glycoprotein complex, which links the cytoskeleton to the extracellular matrix. Defects in several components of this complex cause different types of muscular dystrophy. This glycoprotein complex is also involved in clustering and anchoring acetylcholine receptors at the postsynaptic membrane.
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页码:379 / 384
页数:6
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