POLYSPLENIA AND KARTAGENER SYNDROMES IN A SIBSHIP - ASSOCIATION WITH ABNORMAL RESPIRATORY CILIA

被引:35
作者
SCHIDLOW, DV
KATZ, SM
TURTZ, MG
DONNER, RM
CAPASSO, S
机构
[1] HAHNEMANN MED COLL & HOSP, DEPT PATHOL, PHILADELPHIA, PA 19102 USA
[2] TEMPLE UNIV, ST CHRISTOPHERS HOSP CHILDREN, SCH MED, DEPT OTOLARYNGOL, PHILADELPHIA, PA 19133 USA
关键词
D O I
10.1016/S0022-3476(82)80439-3
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:401 / 403
页数:3
相关论文
共 10 条
[1]   IMMOTILE-CILIA SYNDROME - CONGENITAL CILIARY ABNORMALITY AS AN ETIOLOGIC FACTOR IN CHRONIC AIRWAY INFECTIONS AND MALE-STERILITY [J].
ELIASSON, R ;
MOSSBERG, B ;
CAMNER, P ;
AFZELIUS, BA .
NEW ENGLAND JOURNAL OF MEDICINE, 1977, 297 (01) :1-6
[2]   NORMAL CILIARY ULTRASTRUCTURE IN CHILDREN WITH KARTAGENERS SYNDROME [J].
HERZON, FS ;
MURPHY, S .
ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY, 1980, 89 (01) :81-83
[3]   ULTRASTRUCTURAL FEATURES OF RESPIRATORY CILIA IN CYSTIC-FIBROSIS [J].
KATZ, SM ;
HOLSCLAW, DS .
AMERICAN JOURNAL OF CLINICAL PATHOLOGY, 1980, 73 (05) :682-685
[4]  
LUCAS RV, 1979, BIRTH DEFECTS ATLAS, P583
[5]  
ONGLEY PA, 1965, MAYO CLIN PROC, V40, P609
[6]  
ROSE V, 1975, BRIT HEART J, V37, P840
[7]  
SMITH DW, 1976, RECOGNIZABLE PATTERN, P364
[8]   CILIA WITH DEFECTIVE RADIAL SPOKES - CAUSE OF HUMAN RESPIRATORY-DISEASE [J].
STURGESS, JM ;
CHAO, J ;
WONG, J ;
ASPIN, N ;
TURNER, JAP .
NEW ENGLAND JOURNAL OF MEDICINE, 1979, 300 (02) :53-56
[9]  
VANMIEROP LHS, 1972, BIRTH DEFECTS OAS, V8, P74
[10]  
VANMIEROP LHS, 1979, BIRTH DEFECTS ATLAS, P875