ABNORMALITIES OF THE CORRECTED QT INTERVAL IN FAMILIAL DYSAUTONOMIA - AN INDICATOR OF AUTONOMIC DYSFUNCTION

被引:36
作者
GLICKSTEIN, JS
SCHWARTZMAN, D
FRIEDMAN, D
RUTKOWSKI, M
AXELROD, FB
机构
[1] NYU MED CTR, DEPT PEDIAT, NEW YORK, NY 10016 USA
[2] NYU MED CTR, DIV PEDIAT CARDIOL, NEW YORK, NY 10016 USA
[3] NYU MED CTR, DIV ADULT CARDIOL, NEW YORK, NY 10016 USA
关键词
D O I
10.1016/S0022-3476(09)90022-1
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
We report abnormalities in corrected QT intervals with changes in position and after exercise in patients with familial dysautonomia and confirm the previously reported finding of abnormal heart rate and blood pressure responses. Prolonged corrected QT intervals (>440 msec) with lack of appropriate shortening with exercise is a noninvasive means of demonstrating an aberration in autonomic regulation of cardiac conduction.
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收藏
页码:925 / 928
页数:4
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