COMMON VARIABLE IMMUNODEFICIENCY IN A FAMILY

被引:0
作者
VANSPRONSEN, DJ
KERBERTDRETELER, M
VANDERSLUIJSVEER, G
TENNAPEL, CHH
机构
[1] ZIEKENHUIS ENSCHEDE,MED SPECTRUM TWENTE,DEPT INTERNAL MED,DIV ONCOL AIDS,POB 50000,7500 KA ENSCHEDE,NETHERLANDS
[2] ZIEKENHUIS ENSCHEDE,MED SPECTRUM TWENTE,DEPT CLIN CHEM,IMMUNOL UNIT,7500 KA ENSCHEDE,NETHERLANDS
关键词
HYPOGAMMAGLOBULINEMIA; RECURRENT INFECTION; COMMON VARIABLE IMMUNODEFICIENCY; FAMILIAL;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Common variable immunodeficiency (CVID) is mainly characterised by hypo- or agammaglobulinaemia of late onset, usually discovered in the second decade of life. In individuals CVID is associated with a variable impairment of cellular immunity and the susceptibility to microbial infection may vary as well. CVID is described in a mother and a son who suffered from serious bacterial infections. In addition, minor immunological test abnormalities of apparently healthy first degree relatives are described.
引用
收藏
页码:15 / 22
页数:8
相关论文
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