TYPE-C NIEMANN-PICK DISEASE - LOW-DENSITY LIPOPROTEIN UPTAKE IS ASSOCIATED WITH PREMATURE CHOLESTEROL ACCUMULATION IN THE GOLGI-COMPLEX AND EXCESSIVE CHOLESTEROL STORAGE IN LYSOSOMES

被引：181

作者：

BLANCHETTEMACKIE, EJ

DWYER, NK

AMENDE, LM

KRUTH, HS

BUTLER, JD

SOKOL, J

COMLY, ME

VANIER, MT

AUGUST, JT

BRADY, RO

PENTCHEV, PG

机构：

[1] NHLBI, EXPTL ATHEROSCLEROSIS LAB, BETHESDA, MD 20205 USA

[2] NICHHD, HUMAN GENET BRANCH, BETHESDA, MD 20205 USA

[3] NINCDS, DEV & METAB NEUROL BRANCH, BETHESDA, MD 20205 USA

[4] FAC LYON SUD, BIOCHIM LAB, INSERM, F-69921 OULLINS, FRANCE

[5] JOHNS HOPKINS UNIV, DEPT PHARMACOL & MOLEC SCI, BALTIMORE, MD 21205 USA

来源：

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA | 1988年 / 85卷 / 21期

关键词：

D O I：

10.1073/pnas.85.21.8022

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：8022 / 8026

页数：5

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[10] HETEROGENEOUS DISTRIBUTION OF FILIPIN-CHOLESTEROL COMPLEXES ACROSS THE CISTERNAE OF THE GOLGI-APPARATUS [J].

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