TYPE-C NIEMANN-PICK DISEASE - LOW-DENSITY LIPOPROTEIN UPTAKE IS ASSOCIATED WITH PREMATURE CHOLESTEROL ACCUMULATION IN THE GOLGI-COMPLEX AND EXCESSIVE CHOLESTEROL STORAGE IN LYSOSOMES

被引：181
作者：
BLANCHETTEMACKIE, EJ
DWYER, NK
AMENDE, LM
KRUTH, HS
BUTLER, JD
SOKOL, J
COMLY, ME
VANIER, MT
AUGUST, JT
BRADY, RO
PENTCHEV, PG
机构：
[1] NHLBI, EXPTL ATHEROSCLEROSIS LAB, BETHESDA, MD 20205 USA
[2] NICHHD, HUMAN GENET BRANCH, BETHESDA, MD 20205 USA
[3] NINCDS, DEV & METAB NEUROL BRANCH, BETHESDA, MD 20205 USA
[4] FAC LYON SUD, BIOCHIM LAB, INSERM, F-69921 OULLINS, FRANCE
[5] JOHNS HOPKINS UNIV, DEPT PHARMACOL & MOLEC SCI, BALTIMORE, MD 21205 USA
来源：
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA | 1988年 / 85卷 / 21期
关键词：
D O I：
10.1073/pnas.85.21.8022
中图分类号：
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号：
07 ; 0710 ; 09 ;
摘要：
引用
收藏
页码：8022 / 8026
页数：5
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