Cephalohematoma in a Patient with Ehlers-Danlos Syndrome

被引:0
作者
Felton, Brent M. [1 ,2 ]
White, Josh M. [1 ,2 ]
Jones, Ryan A. [1 ,2 ]
机构
[1] McLaren Greater Lansing Hosp, Dept Emergency Med, Lansing, MI USA
[2] Michigan State Univ, Dept Emergency Med, E Lansing, MI USA
关键词
Cephalhematoma; Ehlers-Danlos; Emergency medicine;
D O I
10.5811/westjem.2013.1.13409
中图分类号
R4 [临床医学];
学科分类号
1002 ; 100602 ;
摘要
Ehlers-Danlos syndrome is a rarely encountered connective tissue disorder characterized by skin hyper-elasticity, joint hyper-flexibility, and vasculature fragility. We report a 41-year-old female presenting with scalp swelling following minor head trauma. The patient presented with a large cephalohematoma that despite compressive measures and Factor IX administration continued to progress, necessitating transfer for definitive surgical intervention. The patient underwent surgical evacuation of approximately 1 liter of blood, followed by drain placement and compression dressing. This case underscores the importance for emergency physicians to recognize the potential vascular catastrophes these patients may present with following even minor injury.
引用
收藏
页码:419 / 420
页数:2
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