MULTICENTRIC ANGIOFOLLICULAR LYMPH-NODE HYPERPLASIA ASSOCIATED WITH MYASTHENIA-GRAVIS

被引:11
作者
PASAOGLU, I
DOGAN, R
TOPCU, M
GUNGEN, Y
机构
[1] HACETTEPE UNIV,FAC MED,DEPT PATHOL,ANKARA 06100,TURKEY
[2] HACETTEPE UNIV,FAC MED,DEPT CHILD HLTH & PEDIAT,PEDIAT NEUROL UNIT,ANKARA 06100,TURKEY
关键词
CASTLEMANS DISEASE; ANGIOFOLLICULAR LYMPH NODE HYPERPLASIA; MYASTHENIA GRAVIS; THYMECTOMY;
D O I
10.1055/s-2007-1016500
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Castleman's disease is often referred to as giant lymph-node hyperplasia. Although this localized disorder most commonly involves the mediastinum, recently many patients have been described with multicentric lymph-node hyperplasia associated with various clinical abnormalities. Here a new case of multicentric angiofollicular lymph-node hyperplasia associated with myasthenia gravis and gammopathy is presented. At first, the patient responded to surgery well, but after some months her condition deteriorated: plasmapheresis was then performed, one year after the operation, with great clinical improvement.
引用
收藏
页码:253 / 256
页数:4
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