SUCCESSFUL TREATMENT OF HOMOZYGOUS PROTEIN-C DEFICIENCY BY HEPATIC TRANSPLANTATION

被引：1
|
作者：
CASELLA, JF
BONTEMPO, FA
MARKEL, H
LEWIS, JH
ZITELLI, BJ
STARZL, TE
机构：
[1] JOHNS HOPKINS UNIV, SCH MED, DEPT ITABASHI KU, DIV HEMATOL, BALTIMORE, MD 21205 USA
[2] CENT BLOOD BANK PITTSBURGH, PITTSBURGH, PA USA
[3] UNIV PITTSBURGH, DEPT MED, PITTSBURGH, PA 15260 USA
[4] UNIV PITTSBURGH, DEPT PEDIAT, PITTSBURGH, PA 15260 USA
[5] UNIV PITTSBURGH, DEPT SURG, PITTSBURGH, PA 15260 USA
来源：
LANCET | 1988年 / 1卷 / 8583期
关键词：
D O I：
暂无
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
A child with homozygous protein C deficiency was treated at age 20 months by orthotopic hepatic transplantation. Postoperatively there was complete reconstitution of protein C activity and resolution of the thrombotic condition.
引用
收藏
页码：435 / 438
页数：4
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