MALIGNANT RENAL TUMORS IN TUBEROUS SCLEROSIS

被引:76
作者
WASHECKA, R [1 ]
HANNA, M [1 ]
机构
[1] NYU MED CTR,DEPT PEDIAT UROL,NEW YORK,NY 10016
关键词
D O I
10.1016/0090-4295(91)80261-5
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
Although the frequency of renal carcinoma in tuberous sclerosis is lower than that in von Hippel-Lindau syndrome, it occurs bilaterally in 43 percent of patients at a median age of twenty-eight years. Concomitant hamartomas and hyperplastic cystic components may confound the histologic diagnosis of renal carcinoma in tuberous sclerosis.
引用
收藏
页码:340 / 343
页数:4
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