A DEFICIENCY OF THE C3B C4B INACTIVATOR (C3B C4BINA) IN 2 SIBLINGS

被引:0
|
作者
ZHU, XJ
OLESKE, J
GIGLI, I
机构
[1] NYU MED CTR,DEPT DERMATOL,NEW YORK,NY 10016
[2] NYU MED CTR,DEPT MED,NEW YORK,NY 10016
[3] COLL MED & DENT NEW JERSEY,DEPT PEDIAT,NEWARK,NJ 07103
来源
CLINICAL RESEARCH | 1982年 / 30卷 / 02期
关键词
D O I
暂无
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:A516 / A516
页数:1
相关论文
共 50 条
  • [21] VARIABLE EXPRESSION OF HOMOZYGOUS C3B INACTIVATOR DEFICIENCY
    ENG, RHK
    SELIGMAN, SJ
    ARNAOUT, MA
    ALPER, CA
    CLINICAL RESEARCH, 1978, 26 (03): : A394 - A394
  • [22] THE C3B INACTIVATOR IS A SERINE PROTEINASE
    HSIUNG, LM
    BARCLAY, AN
    GAGNON, J
    BRANDON, MR
    PORTER, RR
    MOLECULAR IMMUNOLOGY, 1982, 19 (11) : 1376 - 1376
  • [23] MICROHETEROGENEITY AND POLYMORPHISM OF THE C3B/C4B INACTIVATOR-FACTOR-I OF THE HUMAN-COMPLEMENT SYSTEM
    KOLBLE, K
    DIEPGEN, T
    RUKAVINA, V
    WAHN, V
    KALDEN, JR
    IMMUNOBIOLOGY, 1986, 173 (2-5) : 462 - 462
  • [24] INTRACELLULAR DEGRADATION OF THE COMPLEMENT C3B/C4B RECEPTOR IN THE ABSENCE OF LIGAND
    TURNER, JR
    TARTAKOFF, AM
    BERGER, M
    JOURNAL OF BIOLOGICAL CHEMISTRY, 1988, 263 (10) : 4914 - 4920
  • [25] Defining targets for complement components C4b and C3b on the pathogenic neisseriae
    Lewis, Lisa A.
    Ram, Sanjay
    Prasad, Alpana
    Gulati, Sunita
    Getzlaff, Silke
    Blom, Anna M.
    Vogel, Ulrich
    Rice, Peter A.
    INFECTION AND IMMUNITY, 2008, 76 (01) : 339 - 350
  • [26] Effect of immunoglobulin variable region structure on C3b and C4b deposition
    White, KD
    Frank, MB
    Foundling, S
    Waxman, FJ
    MOLECULAR IMMUNOLOGY, 1996, 33 (09) : 759 - 768
  • [27] 2 DIFFERENT COMPLEMENT RECEPTORS ON HUMAN LYMPHOCYTES - ONE SPECIFIC FOR C3B AND ONE SPECIFIC FOR C3B INACTIVATOR-CLEAVED C3B
    ROSS, GD
    POLLEY, MJ
    RABELLINO, EM
    GREY, HM
    JOURNAL OF EXPERIMENTAL MEDICINE, 1973, 138 (04): : 798 - 811
  • [29] HUMAN-COMPLEMENT COMPONENT-C4 - STRUCTURAL STUDIES ON THE FRAGMENTS DERIVED FROM C4B BY CLEAVAGE WITH C3B INACTIVATOR
    PRESS, EM
    GAGNON, J
    BIOCHEMICAL JOURNAL, 1981, 199 (02) : 351 - 357
  • [30] STRUCTURAL CHARACTERIZATION OF THE C3B INACTIVATOR (C3BINA) MEDIATED CLEAVAGE OF HUMAN C-3
    DAVIS, AE
    HARRISON, RA
    MOLECULAR IMMUNOLOGY, 1982, 19 (11) : 1366 - 1366