ABNORMAL LYSOSOMAL CATHEPSIN ACTIVITIES IN LEUKOCYTES AND CULTURED SKIN FIBROBLASTS IN LATE INFANTILE, BUT NOT IN JUVENILE NEURONAL CEROID-LIPOFUSCINOSIS (BATTEN DISEASE)

被引：10
作者：
BENNETT, MJ
CHERN, L
CARPENTER, KH
SLADKY, JT
机构：
[1] CHILDRENS HOSP, DEPT PEDIAT, PHILADELPHIA, PA 19104 USA
[2] CHILDRENS HOSP, DEPT CHEM PATHOL, SHEFFIELD S10 2TH, S YORKSHIRE, ENGLAND
来源：
CLINICA CHIMICA ACTA | 1992年 / 208卷 / 1-2期
关键词：
NEURONAL CEROID-LIPOFUSCINOSIS; BATTEN DISEASE; CATHEPSINS; LYSOSOMAL PROTEASES;
D O I：
10.1016/0009-8981(92)90028-O
中图分类号：
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号：
1001 ;
摘要：
[No abstract available]
引用
收藏
页码：111 / 117
页数：7
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