MACULAR CORNEAL-DYSTROPHY - FAILURE TO SYNTHESIZE A MATURE KERATAN SULFATE PROTEOGLYCAN

被引:167
作者
HASSELL, JR
NEWSOME, DA
KRACHMER, JH
RODRIGUES, MM
机构
[1] UNIV IOWA,DEPT OPHTHALMOL,IOWA CITY,IA 52242
[2] NEI,CLIN BRANCH,OCULAR PATHOL BRANCH,BETHESDA,MD 20014
来源
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES | 1980年 / 77卷 / 06期
关键词
D O I
10.1073/pnas.77.6.3705
中图分类号
Q [生物科学];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:3705 / 3709
页数:5
相关论文
共 29 条
[1]   EXTRACTION AND PURIFICATION OF PROTEOGLYCANS FROM VARIOUS TYPES OF CONNECTIVE-TISSUE [J].
ANTONOPOULOS, CA ;
AXELSSON, I ;
HEINEGARD, D ;
GARDELL, S .
BIOCHIMICA ET BIOPHYSICA ACTA, 1974, 338 (01) :108-119
[2]   CHARACTERIZATION OF KERATAN SULFATE PROTEOGLYCANS FROM BOVINE CORNEAL STROMA [J].
AXELSSON, I ;
HEINEGARD, D .
BIOCHEMICAL JOURNAL, 1978, 169 (03) :517-530
[3]   FRACTIONATION OF PROTEOGLYCANS FROM BOVINE CORNEAL STROMA [J].
AXELSSON, I ;
HEINEGARD, D .
BIOCHEMICAL JOURNAL, 1975, 145 (03) :491-500
[4]   LINKAGE OF CORNEAL KERATAN SULFATE TO PROTEIN [J].
BAKER, JR ;
CIFONELLI, JA ;
RODEN, L .
CONNECTIVE TISSUE RESEARCH, 1975, 3 (2-3) :149-156
[5]  
BRAY BA, 1967, J BIOL CHEM, V242, P3373
[6]   STRUCTURE OF THE LIPID-LINKED OLIGOSACCHARIDES THAT ACCUMULATE IN CLASS-E THY-1-NEGATIVE MUTANT LYMPHOMAS [J].
CHAPMAN, A ;
TROWBRIDGE, IS ;
HYMAN, R ;
KORNFELD, S .
CELL, 1979, 17 (03) :509-515
[7]  
DELUCA S, J BIOL CHEM
[8]  
Francois J, 1966, Trans Ophthalmol Soc U K, V86, P367
[9]  
GARNER A, 1969, INVEST OPHTH VISUAL, V8, P475
[10]  
GOLDBERG MF, 1965, ARCH OPHTHALMOL-CHIC, V74, P516