CONGENITAL ADRENAL-HYPERPLASIA WITH TESTICULAR-TUMORS, AGGRESSION, AND GONADAL FAILURE

被引:13
作者
KEELY, EJ
MATWIJIW, I
THLIVERIS, JA
FAIMAN, C
机构
[1] UNIV MANITOBA, DEPT MED, WINNIPEG R3T 2N2, MANITOBA, CANADA
[2] UNIV MANITOBA, DEPT ANAT, WINNIPEG R3T 2N2, MANITOBA, CANADA
[3] UNIV MANITOBA, DEPT PHYSIOL, WINNIPEG R3T 2N2, MANITOBA, CANADA
[4] HLTH SCI CTR, ENDOCRINOL METAB LAB, WINNIPEG R3E 0W1, MANITOBA, CANADA
关键词
D O I
10.1016/0090-4295(93)90593-Y
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
Bilateral testicular tumors (adrenal rests) may occur in untreated or poorly controlled congenital adrenal hyperplasia. This case report describes two unique associated phenomena: (1) psychologic disturbances similar to those seen with exogenous androgen abuse, which resolved with appropriate glucocorticoid suppression of androgen over-production by this abnormal adrenal/adrenal rest tissue; and (2) testicular failure which showed a partial, delayed recovery with corticosteroid therapy. The need for a careful history and biochemical screening for all patients with bilateral testicular tumors is reinforced.
引用
收藏
页码:346 / 349
页数:4
相关论文
共 16 条
[1]  
BERESFORD TP, 1990, AM J PSYCHIAT, V147, P510
[2]  
BONACCORSI AC, 1987, FERTIL STERIL, V47, P664
[3]   STEROIDOGENIC ENZYME-ACTIVITIES, MORPHOLOGY, AND RECEPTOR STUDIES OF A TESTICULAR ADRENAL REST IN A PATIENT WITH CONGENITAL ADRENAL-HYPERPLASIA [J].
CLARK, RV ;
ALBERTSON, BD ;
MUNABI, A ;
CASSORLA, F ;
AGUILERA, G ;
WARREN, DW ;
SHERINS, RJ ;
LORIAUX, DL .
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM, 1990, 70 (05) :1408-1413
[4]  
CUTFIELD RG, 1983, FERTIL STERIL, V40, P809
[5]   ORGANIC AFFECTIVE-DISORDER IN A PATIENT WITH CONGENITAL ADRENAL-HYPERPLASIA [J].
FELDMAN, SR ;
KRISHNAN, KRR ;
MCPHERSON, H ;
MEGLIN, DE .
BIOLOGICAL PSYCHIATRY, 1987, 22 (06) :767-770
[7]   MASKED 21-HYDROXYLASE DEFICIENCY OF ADRENAL PRESENTING WITH GYNECOMASTIA AND BILATERAL TESTICULAR MASSES [J].
KADAIR, RG ;
BLOCK, MB ;
KATZ, FH ;
HOFELDT, FD .
AMERICAN JOURNAL OF MEDICINE, 1977, 62 (02) :278-282
[8]   HOOKED ON HORMONES - AN ANABOLIC-STEROID ADDICTION HYPOTHESIS [J].
KASHKIN, KB ;
KLEBER, HD .
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1989, 262 (22) :3166-3170
[9]   INFERTILITY IN A MAN WITH 21-HYDROXYLASE DEFICIENT CONGENITAL ADRENAL-HYPERPLASIA [J].
MIRSKY, HA ;
HINES, JH .
JOURNAL OF UROLOGY, 1989, 142 (01) :111-113
[10]  
POPE HG, 1988, AM J PSYCHIAT, V145, P487