DARK-ADAPTATION IN PATIENTS WITH BEST VITELLIFORM MACULAR DYSTROPHY

被引：5

作者：

BACA, W ^{[1
]}

FISHMAN, GA ^{[1
]}

ALEXANDER, KR ^{[1
]}

GLENN, AM ^{[1
]}

机构：

[1] UNIV ILLINOIS,COLL MED,CTR EYE,DEPT OPHTHALMOL & VISUAL SCI,CHICAGO,IL 60612

来源：

BRITISH JOURNAL OF OPHTHALMOLOGY | 1994年 / 78卷 / 06期

关键词：

D O I：

10.1136/bjo.78.6.430

中图分类号：

R77 [眼科学];

学科分类号：

100212 ;

摘要：

Psychophysical dark adaptation studies were performed in six patients with Best vitelliform macular dystrophy (BVMD) using a Goldmann-Weekers dark adaptometer. Prebleach thresholds were determined before obtaining a postbleach full recovery curve. Unlike patients with Stargardt macular dystrophy, all patients with BVMD showed a normal time to reach their baseline dark adapted thresholds after bleaching of their rod visual pigment when tested in clinically normal appearing retina. Although a lipofuscin material accumulates within retinal pigment epithelial cells in patients with either Best or Stargardt dystrophy, functional findings pertaining to recovery of rod dark adaptation thresholds as well as electro-oculogram light peak to dark trough ratios are different in these two disorders.

引用

页码：430 / 432

页数：3

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[41] Optical coherence tomography angiography in best vitelliform macular dystrophy [J].

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[42] Chromatic pupilloperimetry for objective diagnosis of Best vitelliform macular dystrophy [J].

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[43] PROLONGED ROD DARK-ADAPTATION IN PATIENTS WITH CONE-ROD DYSTROPHY [J].

FISHMAN, GA ;

PULLURU, P ;

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DERLACKI, DJ ;

GILBERT, LD .

AMERICAN JOURNAL OF OPHTHALMOLOGY, 1994, 118 (03) :362-367

[44] OCT features in Vitelliform Macular Dystrophy (Best's disease) [J].

Leveziel, N ;

Souied, E ;

Benhamou, N ;

Coscas, G ;

Soubrane, G .

INVESTIGATIVE OPHTHALMOLOGY & VISUAL SCIENCE, 2003, 44 :U711-U711

[45] Unilateral best vitelliform macular dystrophy- a case series [J].

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[46] A Spontaneous Nonhuman Primate Model of Best Vitelliform Macular Dystrophy [J].

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Mai, Xiaomei ;

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Qing, Wenjie ;

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[47] PHOTORECEPTOR INNER SEGMENT MORPHOLOGY IN BEST VITELLIFORM MACULAR DYSTROPHY [J].

Scoles, Drew ;

Sulai, Yusufu N. ;

Cooper, Robert F. ;

Higgins, Brian P. ;

Johnson, Ryan D. ;

Carroll, Joseph ;

Dubra, Alfredo ;

Stepien, Kimberly E. .

RETINA-THE JOURNAL OF RETINAL AND VITREOUS DISEASES, 2017, 37 (04) :741-748

[48] Predominance of hyperopia in autosomal dominant Best vitelliform macular dystrophy [J].

Coussa, Razek G. ;

Binkley, Elaine M. ;

Wilkinson, Mark E. ;

Andorf, Jeaneen L. ;

Tucker, Budd A. ;

Mullins, Robert F. ;

Sohn, Elliott H. ;

Yannuzzi, Lawrence A. ;

Stone, Edwin M. ;

Han, Ian C. .

BRITISH JOURNAL OF OPHTHALMOLOGY, 2022, 106 (04) :522-527

[49] Still no evidence for heterogeneity in Best's vitelliform macular dystrophy [J].

Graff, C ;

Wadelius, C .

JOURNAL OF MEDICAL GENETICS, 1996, 33 (07) :630-630

[50] Lack of evidence for genetic heterogeneity in Best vitelliform macular dystrophy [J].

Mansergh, F ;

Meitinger, T ;

Rodolph, G ;

Humphries, P ;

Farrar, GJ .

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