CHARACTERIZATION OF GLYCOGEN-PHOSPHORYLASE ISOENZYMES PRESENT IN CULTURED SKELETAL-MUSCLE FROM PATIENTS WITH MCARDLES DISEASE

被引:39
作者
SATO, K
IMAI, F
HATAYAMA, I
ROELOFS, RI
机构
[1] HIROSAKI UNIV, SCH MED, DEPT BIOCHEM, HIROSAKI 036, JAPAN
[2] VANDERBILT UNIV, SCH MED, DEPT NEUROL, NASHVILLE, TN 37232 USA
关键词
D O I
10.1016/0006-291X(77)90230-3
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:663 / 668
页数:6
相关论文
共 12 条
[1]   NEW PROGRAM FOR INVESTIGATING ADULT HUMAN SKELETAL-MUSCLE GROWN ANEURALLY IN TISSUE-CULTURE [J].
ASKANAS, V ;
ENGEL, WK .
NEUROLOGY, 1975, 25 (01) :58-67
[2]  
BLOSTEIN R, 1963, J BIOL CHEM, V238, P3280
[3]   ISOENZYME PATTERN OF PHOSPHORYLASE IN WHITE BLOOD-CELLS AND FIBROBLASTS FROM PATIENTS WITH LIVER PHOSPHORYLASE DEFICIENCY [J].
KOSTER, JF ;
SLEE, RG ;
DAEGELEN, D ;
MEIENHOFER, MC ;
DREYFUS, JC ;
NIERMEYER, MF ;
FERNANDES, J .
CLINICA CHIMICA ACTA, 1976, 69 (01) :121-125
[4]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[5]   ISOENZYMES OF GLYCOGEN-PHOSPHORYLASE IN HUMAN AND RABBIT TISSUES .2. ELECTROFOCUSING IN POLYACRYLAMIDE GELS [J].
PROUX, D ;
VIBERT, M ;
MEIENHOFER, MC ;
DREYFUS, JC .
CLINICA CHIMICA ACTA, 1974, 57 (03) :211-216
[6]   PHOSPHORYLASE ISOENZYMES IN TISSUES - PREVALENCE OF LIVER TYPE IN MAN [J].
PROUX, D ;
DREYFUS, JC .
CLINICA CHIMICA ACTA, 1973, 48 (02) :167-172
[7]   HISTOCHEMICAL PHOSPHORYLASE ACTIVITY IN REGENERATING MUSCLE FIBERS FROM MYOPHOSPHORYLASE-DEFICIENT PATIENTS [J].
ROELOFS, RI ;
CHAUVIN, PB ;
ENGEL, WK .
SCIENCE, 1972, 177 (4051) :795-+
[8]   CARCINOFETAL ALTERATIONS IN GLYCOGEN-PHOSPHORYLASE ISOENZYMES IN RAT HEPATOMAS [J].
SATO, K ;
SATO, T ;
MORRIS, HP ;
WEINHOUSE, S .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1975, 259 (AUG22) :273-286
[9]  
SATO K, 1973, CANCER RES, V33, P724
[10]  
SATO K, 1976, CANCER RES, V36, P487