Nevoid Basal Cell Carcinoma Syndrome - Clinical and Radiological Findings of Three Cases

被引：1
|
作者：
Ali, Ibrahim K. [1 ]
Karjodkar, Freny R. [1 ]
Sansare, Kaustubh [1 ]
Salve, Prashant [1 ]
Dora, Amaresh [1 ]
Goyal, Shikha [1 ]
机构：
[1] Nair Hosp, Dent Coll, Oral Med & Radiol, Bombay, Maharashtra, India
来源：
CUREUS | 2016年 / 8卷 / 08期
关键词：
nevoid basal cell carcinoma syndrome; keratocystic odontogenic tumor;
D O I：
10.7759/cureus.727
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Nevoid basal cell carcinoma syndrome (NBCCS) is an autosomal dominant disorder, characterized by skeletal anomalies and multiple keratocystic odontogenic tumors of the jaws. The skeletal anomalies of this syndrome are mandibular prognathism, bossing of frontal and parietal bones, high-arched palate, and bifid rib. We report three cases with NBCCS, emphasizing the clinical and radiographic findings, the importance of the early diagnosis of NBCCS, and a preventive multidisciplinary approach in the management of NBCCS.
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页数：7
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