NON-ALZHEIMERS DISEASE AMYLOIDOSES OF THE NERVOUS-SYSTEM

被引：18
作者：
CASTANO, EM [1 ]
FRANGIONE, B [1 ]
机构：
[1] NEW YORK MED CTR,DEPT PATHOL,NEW YORK,NY
来源：
CURRENT OPINION IN NEUROLOGY | 1995年 / 8卷 / 04期
关键词：
D O I：
10.1097/00019052-199508000-00006
中图分类号：
R74 [神经病学与精神病学];
学科分类号：
摘要：
Amyloidosis and prionosis are disorders of protein conformation. The general mechanisms involved in amyloidogenesis are reviewed here. Recent progress in the molecular pathogenesis of cerebral amyloids is illustrated by three genetic disorders: hereditary amyloid angiopathies of Icelandic and Dutch origins and Gerstmann-Straussler-Scheinker disease.
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页码：279 / 285
页数：7
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