Collapsing variant of focal segmental glomerulosclerosis in children

被引：0

作者：

Nieto Rois, John Fredy ^{[1
]}

Milena Brand, Sandra ^{[3
]}

Serna Higuita, Lina Maria ^{[2
]}

Arias, Luis Fernando ^{[4
]}

机构：

[1] Hosp Pablo Tobon Uribe, Unidad Trasplante Renal & Nefrol, Medellin, Colombia

[2] Hosp Pablo Tobon Uribe, Unidad Trasplante Renal & Nefrol, Nefrol Pediat, Medellin, Colombia

[3] Hosp Pablo Tobon Uribe, Secc Nefrol Pediat, Medellin, Colombia

[4] Univ Antioquia, Serv Patol, Medellin, Colombia

来源：

IATREIA | 2013年 / 26卷 / 04期

关键词：

Glomerulosclerosis; Focal Segmental; Kidney Failure; Chronic; Nephrotic Syndrome;

D O I：

暂无

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

The collapsing variant of focal segmental glomerulosclerosis (FSGS) is a renal lesion that may be idiopathic or associated to different factors; it is characterized by glomerular collapse leading to a nephrotic syndrome resistant to corticosteroids, and chronic progressive renal failure. This glomerulopathy has been scarcely studied in children; in this age group most cases are idiopathic. We report six cases of this variant of FSGS in HIV negative children. They were resistant to the immunosuppressive management and three of them died.

引用

页码：481 / 486

页数：6

共 17 条

[1] Current views on collapsing glomerulopathy [J].

Albaqumi, Mamdouh ;

Barisoni, Laura .

JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY, 2008, 19 (07) :1276-1281

[2] Collapsing glomerulopathy [J].

Albaqumi, Mamdouh ;

Soos, Timothy J. ;

Barisoni, Laura ;

Nelson, Peter J. .

JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY, 2006, 17 (10) :2854-2863

[3] 1Familial collapsing glomerulopathy: Clinical, pathological and immunogenetic features [J].

Avila-Casado, MC ;

Vargas-Alarcon, G ;

Soto, ME ;

Hernandez, G ;

Reyes, PA ;

Herrera-Acosta, J .

KIDNEY INTERNATIONAL, 2003, 63 (01) :233-239

[4] Pathologic classification of focal segmental glomerulosclerosis: A working proposal [J].

D'Agati, VD ;

Fogo, AB ;

Bruijn, JA ;

Jennette, JC .

AMERICAN JOURNAL OF KIDNEY DISEASES, 2004, 43 (02) :368-382

[5] Idiopathic collapsing focal segmental glomerulosclerosis in pediatric patients [J].

El-Refaey, Ahmed M. ;

Kapur, Gaurav ;

Jain, Amrish ;

Hidalgo, Guillermo ;

Imam, Abubakr ;

Valentini, Rudolph P. ;

Mattoo, Tej K. .

PEDIATRIC NEPHROLOGY, 2007, 22 (03) :396-402

[6] Primary focal segmental glomerulosclerosis in Egyptian children: a 10-year single-centre experience [J].

El-Refaey, Ahmed M. ;

Bakr, Ashraf ;

Hammad, Ayman ;

Elmougy, Atef ;

El-Houseeny, Fatma ;

Abdelrahman, Ashraf ;

Sarhan, Amr .

PEDIATRIC NEPHROLOGY, 2010, 25 (07) :1369-1373

[7] Idiopathic collapsing glomerulopathy in children [J].

Gulati, Ashima ;

Sharma, Alok ;

Hari, Pankaj ;

Dinda, Amit K. ;

Bagga, Arvind .

CLINICAL AND EXPERIMENTAL NEPHROLOGY, 2008, 12 (05) :348-353

[8] Collapsing glomerulopathy: Many means to a similar end [J].

Haas, M. .

KIDNEY INTERNATIONAL, 2008, 73 (06) :669-671

[9] Primary focal segmental glomerular sclerosis in children: clinical course and prognosis [J].

Paik, Kyung Hoon ;

Lee, Bum Hee ;

Cho, Hee Yeon ;

Kang, Hee Gyung ;

Ha, Il Soo ;

Cheong, Hae Il ;

Jin, Dong-Kyu ;

Moon, Kyung Chul ;

Choi, Yong .

PEDIATRIC NEPHROLOGY, 2007, 22 (03) :389-395

[10] Remission of proteinuria in primary glomerulonephritis: we know the goal but do we know the price? [J].

Philibert, David ;

Cattran, Daniel .

NATURE CLINICAL PRACTICE NEPHROLOGY, 2008, 4 (10) :550-559

← 1 2 →