JUVENILE DISTAL SPINAL MUSCULAR-ATROPHY OF UPPER EXTREMITIES IN CHINESE MALES - A SINGLE FIBER ELECTROMYOGRAPHIC STUDY OF ARMS AND LEGS

被引:21
作者
CHAN, YW
KAY, R
SCHWARTZ, MS
机构
[1] CHINESE UNIV HONG KONG,SHA TIN,HONG KONG
[2] KWONG WAH HOSP,DEPT MED,HONG KONG,HONG KONG
关键词
D O I
10.1136/jnnp.54.2.165
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Single fibre electromyography (SFEMG) was performed on six young Chinese males with distal spinal muscular atrophy of the upper extremities. Abnormal SFEMG findings of increased fibre density, jitter and blocking were recorded over both arms and legs in all patients, suggesting a more generalised disturbance than would appear clinically.
引用
收藏
页码:165 / 166
页数:2
相关论文
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