PROSPECTS FOR GENE-THERAPY OF FAMILIAL HYPERCHOLESTEROLEMIA

被引:0
作者
WILSON, JM
CHOWDHURY, JR
机构
[1] UNIV MICHIGAN,HOWARD HUGHES MED INST,DEPT BIOL CHEM,ANN ARBOR,MI 48109
[2] YESHIVA UNIV ALBERT EINSTEIN COLL MED,LIVER RES CTR,DEPT INTERNAL MED,BRONX,NY 10461
关键词
D O I
暂无
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:223 / 232
页数:10
相关论文
共 56 条
[1]   CARBOHYDRATE-SPECIFIC RECEPTORS OF THE LIVER [J].
ASHWELL, G ;
HARFORD, J .
ANNUAL REVIEW OF BIOCHEMISTRY, 1982, 51 :531-554
[2]   LIVER-TRANSPLANTATION TO PROVIDE LOW-DENSITY-LIPOPROTEIN RECEPTORS AND LOWER PLASMA-CHOLESTEROL IN A CHILD WITH HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIA [J].
BILHEIMER, DW ;
GOLDSTEIN, JL ;
GRUNDY, SM ;
STARZL, TE ;
BROWN, MS .
NEW ENGLAND JOURNAL OF MEDICINE, 1984, 311 (26) :1658-1664
[3]   IMPAIRED RECEPTOR-MEDIATED CATABOLISM OF LOW-DENSITY LIPOPROTEIN IN THE WHHL RABBIT, AN ANIMAL-MODEL OF FAMILIAL HYPERCHOLESTEROLEMIA [J].
BILHEIMER, DW ;
WATANABE, Y ;
KITA, T .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (10) :3305-3309
[4]  
BILHEIMER DW, 1989, ARTERIOSCLER, V9, P158
[5]   A RECEPTOR-MEDIATED PATHWAY FOR CHOLESTEROL HOMEOSTASIS [J].
BROWN, MS ;
GOLDSTEIN, JL .
SCIENCE, 1986, 232 (4746) :34-47
[6]  
DAVIS CG, 1987, J BIOL CHEM, V262, P4075
[7]   REPLACEMENT OF LIVER-FUNCTION IN RATS BY TRANSPLANTATION OF MICROCARRIER-ATTACHED HEPATOCYTES [J].
DEMETRIOU, AA ;
WHITING, JF ;
FELDMAN, D ;
LEVENSON, SM ;
CHOWDHURY, NR ;
MOSCIONI, AD ;
KRAM, M ;
CHOWDHURY, JR .
SCIENCE, 1986, 233 (4769) :1190-1192
[8]   NEW METHOD OF HEPATOCYTE TRANSPLANTATION AND EXTRACORPOREAL LIVER SUPPORT [J].
DEMETRIOU, AA ;
WHITING, J ;
LEVENSON, SM ;
CHOWDHURY, NR ;
SCHECHNER, R ;
MICHALSKI, S ;
FELDMAN, D ;
CHOWDHURY, JR .
ANNALS OF SURGERY, 1986, 204 (03) :259-271
[9]   SURVIVAL, ORGANIZATION, AND FUNCTION OF MICROCARRIER-ATTACHED HEPATOCYTES TRANSPLANTED IN RATS [J].
DEMETRIOU, AA ;
LEVENSON, SM ;
NOVIKOFF, PM ;
NOVIKOFF, AB ;
CHOWDHURY, NR ;
WHITING, J ;
REISNER, A ;
CHOWDHURY, JR .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1986, 83 (19) :7475-7479
[10]   INTRODUCTION OF A SELECTABLE GENE INTO PRIMITIVE STEM-CELLS CAPABLE OF LONG-TERM RECONSTITUTION OF THE HEMATOPOIETIC SYSTEM OF W/WV MICE [J].
DICK, JE ;
MAGLI, MC ;
HUSZAR, D ;
PHILLIPS, RA ;
BERNSTEIN, A .
CELL, 1985, 42 (01) :71-79