DIAGNOSIS AND TREATMENT OF HOMOZYGOUS PROTEIN-C DEFICIENCY

被引:202
|
作者
MARLAR, RA
MONTGOMERY, RR
BROEKMANS, AW
机构
[1] UNIV COLORADO, HLTH SCI CTR, DEPT BIOCHEM, DENVER, CO 80262 USA
[2] UNIV COLORADO, HLTH SCI CTR, DEPT GENET, DENVER, CO 80262 USA
[3] VET ADM MED CTR, DENVER, CO 80220 USA
[4] BLOOD CTR SE WISCONSIN, MILWAUKEE, WI USA
[5] STATE UNIV LEIDEN HOSP, HEMOSTASIS & THROMBOSIS RES UNIT, 2333 AA LEIDEN, NETHERLANDS
来源
JOURNAL OF PEDIATRICS | 1989年 / 114卷 / 04期
关键词
D O I
10.1016/S0022-3476(89)80688-2
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:528 / 534
页数:7
相关论文
共 50 条
  • [31] REPLACEMENT THERAPY FOR A HOMOZYGOUS PROTEIN-C DEFICIENCY-STATE USING A CONCENTRATE OF HUMAN PROTEIN-C AND PROTEIN-S
    VUKOVICH, T
    AUBERGER, K
    WEIL, J
    ENGELMANN, H
    KNOBL, P
    HADORN, HB
    BRITISH JOURNAL OF HAEMATOLOGY, 1988, 70 (04) : 435 - 440
  • [32] TREATMENT OF PROTEIN-C DEFICIENCY WITH A MONOCLONAL-ANTIBODY PURIFIED PROTEIN-C CONCENTRATE
    SCHWARZ, HP
    LINNAU, Y
    SCHRAMM, W
    DREYFUS, M
    BAUER, KA
    ARTERIOSCLEROSIS, 1990, 10 (05): : A891 - A891
  • [33] TREATMENT OF HEREDITARY PROTEIN-C DEFICIENCY WITH STANOZOLOL
    BROEKMANS, AW
    CONARD, J
    VANWEYENBERG, RG
    HORELLOU, MH
    KLUFT, C
    BERTINA, RM
    THROMBOSIS AND HAEMOSTASIS, 1987, 57 (01) : 20 - 24
  • [34] PROTEIN-C DEFICIENCY
    RAPPAPORT, ES
    SPEIGHTS, VO
    HELBERT, B
    TROWBRIDGE, A
    KOOPS, B
    MONTGOMERY, RR
    MARLAR, RA
    SOUTHERN MEDICAL JOURNAL, 1987, 80 (02) : 240 - 242
  • [35] PRENATAL-DIAGNOSIS OF HEREDITARY PROTEIN-C DEFICIENCY
    MIBASHAN, RS
    MILLAR, DS
    RODECK, CH
    NICOLAIDES, KH
    BERGER, A
    SELIGSOHN, U
    NEW ENGLAND JOURNAL OF MEDICINE, 1985, 313 (25): : 1607 - 1607
  • [36] PROTEIN-C DEFICIENCY
    RAPPAPORT, ES
    SPEIGHTS, VO
    HELBERT, B
    TROWBRIDGE, A
    KOOPS, B
    MONTGOMERY, RR
    MARLAR, RA
    SOUTHERN MEDICAL JOURNAL, 1986, 79 (02) : 44 - 44
  • [37] PROTEIN-C DEFICIENCY
    SCHARRER, I
    DEUTSCHE MEDIZINISCHE WOCHENSCHRIFT, 1995, 120 (13) : 462 - 462
  • [38] COUMARIN PROPHYLAXIS FOR FULMINANT PURPURA SYNDROME DUE TO HOMOZYGOUS PROTEIN-C DEFICIENCY
    GARCIAPLAZA, I
    JIMENEZASTORGA, C
    BORREGO, D
    MARTY, ML
    LANCET, 1985, 1 (8429): : 634 - 635
  • [39] COMPARISON OF 3 FUNCTIONAL PROTEIN C ASSAYS FOR DIAGNOSIS OF PROTEIN-C DEFICIENCY IN PATIENTS ON ORAL ANTICOAGULANT TREATMENT
    PABINGER, I
    KYRLE, P
    SPEISER, W
    STOFFELS, U
    EICHINGER, S
    LECHNER, K
    THROMBOSIS AND HAEMOSTASIS, 1989, 62 (01) : 441 - 441
  • [40] PROTEIN-C CONCENTRATE IN THE TREATMENT OF WARFARIN-INDUCED SKIN NECROSIS IN THE PROTEIN-C DEFICIENCY
    LEWANDOWSKI, K
    ZAWILSKA, K
    THROMBOSIS AND HAEMOSTASIS, 1994, 71 (03) : 395 - 395