MALIGNANT MELANOTIC NEUROECTODERMAL TUMOR OF INFANCY

被引:26
作者
DAMMANN, O
HAGEL, C
ALLERS, B
GRUBEL, G
SCHULTE, FJ
机构
[1] UNIV HAMBURG,KRANKENHAUS EPPENDORF,INST PATHOL,NEUROPATHOL ABT,D-20246 HAMBURG,GERMANY
[2] UNIV HAMBURG,KRANKENHAUS EPPENDORF,NEUROL KLIN & POLIKLIN,NEUROCHIRURG ABT,D-20246 HAMBURG,GERMANY
关键词
MALIGNANT MELANOTIC NEUROECTODERMAL TUMOR OF INFANCY; CHILDHOOD; NEUROPSYCHOLOGICAL FOLLOW-UP;
D O I
10.1007/BF00570263
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 2-month-old boy underwent surgery for removal of a right temporal melanotic neuroectodermal tumor of infancy (MNTI). Histologically the tumor tissue showed signs of malignancy. The child was reexamined several times up to the age of 5 years. Neuroradiological evaluation showed no evidence of tumor recurrence or metastases. No resulting handicap was observed during neurological and psychological follow-up examination at the age of 5 years. Our findings confirm that surgical removal as the therapy of choice provides an excellent prognosis for this kind of tumor in spite of its histologically malignant appearance.
引用
收藏
页码:186 / 188
页数:3
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