Klippel-Trenaunay Syndrome: A Rare Cause of Recurrent Lower GI Bleeding

Klippel-Trenaunay syndrome is a non-hereditary congenital abnormality characterized by a clinical triad of soft tissue hypertrophy of an extremity, varicosities and cutaneous hemangiomas or Lymhangiomas. Hematochezia is an uncommon but potentially serious complication of Klippel-Trenaunay syndrome. We report here a case of a young female who presented to us with intermittent bleeding per rectum and iron deficiency anemia. The patient gave history of excision of hemangioma in the right leg 12years ago. Her upper GI endoscopy revealed grade-I esophageal varices and colonoscopy showed vascular malformation from rectum to sigmoid. CT Angio revealed splenic haemangiomas with multiple vascular malformations in GI tract.