ADJUVANT CHEMOTHERAPY FOR TREATMENT OF UNRESECTABLE AND METASTATIC ANGIOMATOID MALIGNANT FIBROUS HISTIOCYTOMA

被引:1
作者
BERNINI, JC
FORT, DW
PRITCHARD, M
ROGERS, BB
WINICK, NJ
机构
[1] UNIV TEXAS,SW MED CTR,DEPT PEDIAT HEMATOL ONCOL,DALLAS,TX
[2] UNIV TEXAS,SW MED CTR,DEPT RADIOL,DALLAS,TX 75235
[3] UNIV TEXAS,SW MED CTR,DEPT PATHOL,DALLAS,TX
[4] CHILDRENS MED CTR,DALLAS,TX 75235
关键词
ANGIOMATOID MALIGNANT FIBROUS HISTIOCYTOMA; MALIGNANT FIBROUS HISTIOCYTOMA; SARCOMA; CHILDREN;
D O I
10.1002/1097-0142(19940801)74:3<962::AID-CNCR2820740327>3.0.CO;2-A
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Angiomatoid malignant fibrous histiocytoma (AMFH) is a low grade soft tissue sarcoma usually treated with surgery alone. Only one adult patient has been treated with systemic chemotherapy. The authors report a case of unresectable, metastatic AMFH treated initially with vincristine, doxorubicin, dactinomycin, and cyclophosphamide. A complete response at the metastatic site and a marked reduction in the size of the primary tumor allowed complete surgical excision 7 months after treatment was initiated. The patient remains disease free 19 months after being diagnosed. It was concluded that systemic chemotherapy may be effective in patients with AMFH.
引用
收藏
页码:962 / 964
页数:3
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