CARDIAC TUMORS IN TUBEROUS SCLEROSIS - THEIR INCIDENCE AND COURSE

被引:55
作者
JOZWIAK, S [1 ]
KAWALEC, W [1 ]
DLUZEWSKA, J [1 ]
DASZKOWSKA, J [1 ]
MIRKOWICZMALEK, M [1 ]
MICHALOWICZ, R [1 ]
机构
[1] CHILDS HLTH CTR,DEPT CARDIOL,PL-04736 WARSAW,POLAND
关键词
TUBEROUS SCLEROSIS; CARDIAC TUMORS; ECHOCARDIOGRAPHY; CHILDREN;
D O I
10.1007/s004310050110
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Cardiac tumours have been frequently reported in patients with tuberous sclerosis but their incidence at different ages has been evaluated in only a few studies. We performed echocardiography in 47 children with tuberous sclerosis and found tumours in 22 (47%). In none, except one newborn, did we observe any clinical symptoms of heart failure. Tumours were more frequent in children below 2 years of age (91%) than in older children. As other signs of tuberous sclerosis are often absent in infants, echocardiography may be regarded as the most useful diagnostic test at this age. Follow up studies were done in 12 children and tumour regression occurred in 6 patients.
引用
收藏
页码:155 / 157
页数:3
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