QUANTITATIVE ASSESSMENT OF SCANNING ELECTRON-MICROSCOPE DEFECTS IN UNCOMBABLE-HAIR SYNDROME

被引：23

作者：

REST, EB ^{[1
]}

FRETZIN, DF ^{[1
]}

机构：

[1] RUSH PRESBYTERIAN ST LUKES MED CTR,DEPT DERMATOL,CHICAGO,IL 60612

来源：

PEDIATRIC DERMATOLOGY | 1990年 / 7卷 / 02期

关键词：

D O I：

10.1111/j.1525-1470.1990.tb00661.x

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

Abstract: Uncombable‐hair syndrome is a rare disorder of scalp hair that starts early in childhood. It is characterized clinically as unruly hair and by scanning electron microscopy as longitudinally grooved hairs with a triangular cross section. Because of the controversy of inheritance and prior reports of similar changes in normal and other hair disorders, we performed a quantitative scanning electron microscopic assessment of four patients with uncombable‐hair syndrome, first‐degree relatives, and nonaffected controls. Our results indicate that longitudinal grooving of scalp hair is a common occurrence, and that for clinical changes to be apparent, approximately 50% of hairs must be affected. Copyright © 1990, Wiley Blackwell. All rights reserved

引用

页码：93 / 96

页数：4

共 27 条

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