Granular cell tumor is a rare benign tumor which when affects the larynx, it characteristically affects the vocal cords, causing dysphonia as the main clinical manifestation. The term granular cell myoblastoma proposed and extensively used seems to be inadequate since all the observations suggest its origin in Schwann cells, with no relation to muscle cells. Although the existence of malignant granular cell tumors has been reported, the vast majority show a benign behaviour, reaching its cure after complete surgical removal of the lesion.