KINETIC-ANALYSIS OF ARGININOSUCCINATE SYNTHETASE IN A VARIANT FORM OF CITRULLINEMIA

被引:15
作者
AKABOSHI, I [1 ]
ENDO, F [1 ]
MATSUDA, I [1 ]
SAHEKI, T [1 ]
机构
[1] KAGOSHIMA UNIV,SCH MED,DEPT BIOCHEM,KAGOSHIMA 890,JAPAN
关键词
D O I
10.1007/BF02391191
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:36 / 39
页数:4
相关论文
共 10 条
[1]  
AKIGUCHI I, 1978, TAISHIA, V7, P1057
[2]   CITRULLINEMIA - ENZYMATIC EVIDENCE FOR GENETIC-HETEROGENEITY [J].
KENNAWAY, NG ;
HARWOOD, PJ ;
RAMBERG, DA ;
KOLER, RD ;
BUIST, NRM .
PEDIATRIC RESEARCH, 1975, 9 (06) :554-558
[3]   LYSINE INTOLERANCE IN A VARIANT FORM OF CITRULLINEMIA [J].
MATSUDA, I ;
ARASHIMA, S ;
IMANISHI, Y ;
YAMAMOTO, J ;
AKABOSHI, I ;
SHINOZUKA, S ;
NAGATA, N .
PEDIATRIC RESEARCH, 1979, 13 (10) :1134-1136
[4]   VARIANT FORM OF CITRULLINEMIA [J].
MATSUDA, I ;
ANAKURA, M ;
ARASHIMA, S ;
SAITO, Y ;
OKA, Y .
JOURNAL OF PEDIATRICS, 1976, 88 (05) :824-826
[5]   STUDIES ON LIVER ARGININOSUCCINATE SYNTHETASE IN A PATIENT WITH CITRULLINEMIA AND IN NORMAL SUBJECTS [J].
MATSUDA, Y ;
TSUJI, A ;
KATUNUMA, N ;
HAYASHI, M ;
TAKAHASHI, Y .
JOURNAL OF BIOCHEMISTRY, 1979, 85 (01) :191-195
[6]  
MCMURRAY WC, 1963, PEDIATRICS, V32, P347
[7]   QUALITATIVE AND QUANTITATIVE ABNORMALITIES OF ARGININOSUCCINATE SYNTHETASE IN CITRULLINEMIA [J].
SAHEKI, T ;
UEDA, A ;
HOSOYA, M ;
KUSUMI, K ;
TAKADA, S ;
TSUDA, M ;
KATSUNUMA, T .
CLINICA CHIMICA ACTA, 1981, 109 (03) :325-335
[8]  
SCHMIKE RT, 1962, J BIOL CHEM, V237, P459
[9]  
SCHMIKE RT, 1964, J BIOL CHEM, V239, P136
[10]   CITRULLINAEMIA WITH RAPIDLY FATAL NEONATAL COURSE [J].
VANDERZEE, SP ;
TRIJBELS, JM ;
MONNENS, LAH ;
HOMMES, FA ;
SCHRETLE.DA .
ARCHIVES OF DISEASE IN CHILDHOOD, 1971, 46 (250) :847-+