IDENTIFICATION OF THE MAJOR 4-METHYLUMBELLIFERYL PARA-GUANIDINOBENZOATE-HYDROLYZING PLASMA-PROTEIN IN CYSTIC-FIBROSIS - IMPLICATION FOR INTRAUTERINE AND HETEROZYGOTE DETECTION

被引：2
作者：
BRANCHINI, BR
SALITURO, GM
ROSENSTEIN, BJ
机构：
[1] JOHNS HOPKINS UNIV, DEPT CHEM, BALTIMORE, MD 21218 USA
[2] JOHNS HOPKINS UNIV, SCH MED, DEPT PEDIAT, BALTIMORE, MD 21205 USA
来源：
PEDIATRIC RESEARCH | 1983年 / 17卷 / 11期
关键词：
D O I：
10.1203/00006450-198311000-00003
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
引用
收藏
页码：850 / 855
页数：6
相关论文
共 37 条
[1]  
BRANCHINI BR, 1982, LANCET, V1, P618
[2]  
BRANCHINI BR, UNPUB
[3]  
BROCK DJH, 1982, LANCET, V1, P619
[4]   SENSITIVE FLUORESCENT DETERMINATION OF TRYPSIN-LIKE PROTEASES [J].
BROWN, F ;
FREEDMAN, ML ;
TROLL, W .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1973, 53 (01) :75-81
[5]  
BRUNO JJ, 1969, FED PROC, V28, P840
[6]   PLASMA ARGININE ESTERASE IN CYSTIC-FIBROSIS - KINETICS OF ACTIVATION, IDENTIFICATION AS PLASMA KALLIKREIN, REACTION WITH ALPHA-2-MACROGLOBULIN AND COMPARISON WITH LEVELS IN NORMAL PLASMA [J].
BURY, AF ;
BARRETT, AJ .
PEDIATRIC RESEARCH, 1982, 16 (08) :613-620
[7]   REACTION OF PLASMA ALBUMIN WITH I-NAPHTHYL N-METHYLCARBAMATE AND CERTAIN OTHER ESTERS [J].
CASIDA, JE ;
AUGUSTINSSON, KB .
BIOCHIMICA ET BIOPHYSICA ACTA, 1959, 36 (02) :411-426
[8]   CYSTIC-FIBROSIS AND MALNUTRITION [J].
CHASE, HP ;
LONG, MA ;
LAVIN, MH .
JOURNAL OF PEDIATRICS, 1979, 95 (03) :337-347
[9]   STUDIES ON PREKALLIKREIN (KALLIKREINOGEN)-KALLIKREIN ENZYME SYSTEM OF HUMAN PLASMA .2. EVIDENCE RELATING KAOLIN-ACTIVATED ARGININE ESTERASE TO PLASMA KALLIKREIN [J].
COLMAN, RW ;
MATTLER, L ;
SHERRY, S .
JOURNAL OF CLINICAL INVESTIGATION, 1969, 48 (01) :23-&
[10]  
DANN LG, 1982, LANCET, V1, P619
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