HETEROGENEITY IN THE MOLECULAR-BASIS OF 3 TYPES OF HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN AND THE RELATIVE SYNTHESIS OF THE G-GAMMA-TYPE AND A-GAMMA-TYPE OF GAMMA-CHAIN

被引:66
作者
KUTLAR, A
GARDINER, MB
HEADLEE, MG
REESE, AL
CLEEK, MP
NAGLE, S
SUKUMARAN, PK
HUISMAN, IHJ
机构
[1] MED COLL GEORGIA,DEPT CELL & MOLEC BIOL,CTR COMPREHENS SICKLE CELL,AUGUSTA,GA 30912
[2] MED COLL GEORGIA,DEPT CELL & MOLEC BIOL,PROT CHEM LAB,AUGUSTA,GA 30912
[3] VET ADM MED CTR,MED RES SERV,AUGUSTA,GA 30910
关键词
D O I
10.1007/BF00499284
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:21 / 35
页数:15
相关论文
共 26 条
[1]  
ABRAHAM E C, 1976, Hemoglobin, V1, P27, DOI 10.3109/03630267609031020
[2]  
BERNARDS R, 1980, NUCLEIC ACIDS RES, V8, P1521, DOI 10.1093/nar/8.7.1521
[3]   ESTIMATION OF SMALL PERCENTAGES OF FOETAL HAEMOGLOBIN [J].
BETKE, K ;
MARTI, HR ;
SCHLICHT, I .
NATURE, 1959, 184 (4702) :1877-1878
[4]   NEGRO VARIETY OF HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN IS A MILD FORM OF THALASSEMIA [J].
CHARACHE, S ;
CLEGG, JB ;
WEATHERALL, DJ .
BRITISH JOURNAL OF HAEMATOLOGY, 1976, 34 (04) :527-534
[5]   GAMMA-CHAIN HETEROGENEITY OF FETAL HEMOGLOBIN IN NON-BLACK BETA-THALASSEMIA AND DELTA-BETA-THALASSEMIA AND HPFH HETEROZYGOTES AND HOMOZYGOTES [J].
EFREMOV, GD ;
IBARRA, B ;
GURGEY, A ;
SUKUMARAN, PK ;
ALTAY, C ;
HUISMAN, THJ .
AMERICAN JOURNAL OF HEMATOLOGY, 1982, 12 (04) :367-382
[6]   THE DISTRIBUTION OF FETAL HEMOGLOBIN AND THE TYPES OF GAMMA-CHAIN IN RED-CELL FRACTIONS SEPARATED BY GRADIENT CENTRIFUGATION FROM BLOOD OF PATIENTS WITH SICKLE-CELL-ANEMIA AND OTHER HEMOGLOBINOPATHIES [J].
HEADLEE, ME ;
GARDINER, MB ;
REESE, AL ;
HUISMAN, THJ .
BIOCHEMICAL MEDICINE, 1983, 29 (03) :337-354
[7]  
HUISMAN THJ, 1981, BLOOD, V57, P75
[8]   HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN - HETEROGENEITY OF FETAL HEMOGLOBIN IN HOMOZYGOTES AND IN CONJUNCTION WITH BETA-THALASSEMIA [J].
HUISMAN, THJ ;
SHELTON, JB ;
SCHROEDER, WA ;
CHARACHE, S ;
BETHLENFALVAY, NC ;
BOUVER, N ;
SHELTON, JR ;
APELL, G .
NEW ENGLAND JOURNAL OF MEDICINE, 1971, 285 (13) :711-+
[9]   EVIDENCE FOR MULTIPLE STRUCTURAL GENES FOR GAMMA-CHAIN OF HUMAN FETAL HEMOGLOBIN IN HEREDITARY PERSISTENCE OF FETAL HEMOGLOBIN [J].
HUISMAN, THJ ;
SCHROEDER, WA ;
DOZY, AM ;
SHELTON, JR ;
SHELTON, JB ;
BOYD, EM ;
APELL, G .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1969, 165 (A1) :320-+
[10]   PRESENT STATUS OF HETEOGENEITY OF FETAL HEMOGLOBIN IN BETA-THALASSEMIA - ATTEMPT TO UNIFY SOME OBSERVATIONS IN THALASSEMIA AND RELATED CONDITIONS [J].
HUISMAN, THJ ;
SCHROEDER, WA ;
EFREMOV, GD ;
DUMA, H ;
MLADENOVSKI, B ;
HYMAN, CB ;
RACHMILEWITZ, EA ;
BOUVER, N ;
MILLER, A ;
BRODIE, A ;
SHELTON, JR ;
SHELTON, JB ;
APELL, G .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1974, 232 (MAY24) :107-124