LARSEN SYNDROME - REVIEW OF THE LITERATURE AND ANALYSIS OF 38 CASES

被引：44
作者：
LAVILLE, JM
LAKERMANCE, P
LIMOUZY, F
机构：
[1] Service de Chirurgie Infantile, C.H.D. Félix Guyon, He de la Reunion
来源：
JOURNAL OF PEDIATRIC ORTHOPAEDICS | 1994年 / 14卷 / 01期
关键词：
CONGENITAL DISLOCATION OF THE KNEE; HYPERELASTICITY; LARSEN SYNDROME; MULTIPLE JOINT DISLOCATION; NANISM;
D O I：
10.1097/01241398-199401000-00014
中图分类号：
R826.8 [整形外科学]; R782.2 [口腔颌面部整形外科学]; R726.2 [小儿整形外科学]; R62 [整形外科学（修复外科学）];
学科分类号：
摘要：
Thirty-eight cases of Larsen's syndrome in patients living on Reunion Island were analyzed, with an average follow-up of 13 years. Fourteen of these patients died of early complications secondary to dislocation of the cervical spine, tracheomalacias, heart disease, and severe respiratory infection. These children pose a problem of planning early treatment. Clubfeet must be treated conservatively early, and operation should be postponed until after knee deformities are corrected by plaster cast and/or early operation. Unilateral hip dislocations should be treated surgically in the second year of life. Treatment of bilateral hip dislocations is best neglected. Finally, the spinal status of these children must be monitored throughout their life.
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页码：63 / 73
页数：11
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