ACTIVATION OF BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE COMPLEX BY ALPHA-CHLOROISOCAPROATE IN NORMAL AND ENZYME-DEFICIENT FIBROBLASTS

被引:10
作者
TOSHIMA, K
KURODA, Y
YOKOTA, I
NAITO, E
ITO, M
WATANABE, T
TAKEDA, E
MIYAO, M
机构
关键词
D O I
10.1016/0009-8981(85)90070-1
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
引用
收藏
页码:103 / 108
页数:6
相关论文
共 10 条
[1]   ACTIVITIES OF BRANCHED-CHAIN 2-OXO ACID DEHYDROGENASE AND ITS COMPONENTS IN SKIN FIBROBLASTS FROM NORMAL AND "CLASSICAL-MAPLE-SYRUP-URINE-DISEASE SUBJECTS [J].
CHUANG, DT ;
NIU, WL ;
COX, RP .
BIOCHEMICAL JOURNAL, 1981, 200 (01) :59-67
[2]   PURIFICATION AND PROPERTIES OF BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASE PHOSPHATASE FROM BOVINE KIDNEY [J].
DAMUNI, Z ;
MERRYFIELD, ML ;
HUMPHREYS, JS ;
REED, LJ .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1984, 81 (14) :4335-4338
[3]   ENZYME-ACTIVITY IN CLASSICAL AND VARIANT FORMS OF MAPLE SYRUP URINE DISEASE [J].
DANCIS, J ;
COX, RP ;
SNYDERMAN, SE ;
HUTZLER, J .
JOURNAL OF PEDIATRICS, 1972, 81 (02) :312-+
[4]   ACTIVITY STATE OF THE BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE COMPLEX IN HEART, LIVER, AND KIDNEY OF NORMAL, FASTED, DIABETIC, AND PROTEIN-STARVED RATS [J].
GILLIM, SE ;
PAXTON, R ;
COOK, GA ;
HARRIS, RA .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1983, 111 (01) :74-81
[5]  
HARRIS RA, 1982, J BIOL CHEM, V257, P3915
[6]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[7]  
PAXTON R, 1982, J BIOL CHEM, V257, P4433
[8]  
RANDLE PJ, 1981, METABOLISM CLIN IMPL, P13
[9]  
SAKAGUCHI Y, 1983, NIHON SHONIKA GAKKAI, V87, P2426
[10]  
Tanaka K, 1983, METABOLIC BASIS INHE, P440