ABNORMAL RESPIRATORY EPITHELIAL ION-TRANSPORT IN CYSTIC-FIBROSIS

被引:0
作者
KNOWLES, MR [1 ]
STUTTS, MJ [1 ]
YANKASKAS, JR [1 ]
GATZY, JT [1 ]
BOUCHER, RC [1 ]
机构
[1] UNIV N CAROLINA, TOXICOL & PHARMACOL, CHAPEL HILL, NC 27514 USA
关键词
D O I
暂无
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
引用
收藏
页码:285 / 297
页数:13
相关论文
共 50 条
[31]   CYSTIC-FIBROSIS AND MEMBRANE TRANSPORT [J].
DUFFY, MJ ;
SCHWARZ, V .
LANCET, 1972, 2 (7768) :136-&
[32]   CYSTIC-FIBROSIS - A TRANSPORT PROBLEM [J].
RINGE, D ;
PETSKO, GA .
NATURE, 1990, 346 (6282) :312-313
[33]   PERSISTENCE OF ABNORMAL CHLORIDE-ION PERMEABILITY IN CYSTIC-FIBROSIS NASAL EPITHELIAL-CELLS IN HETEROLOGOUS CULTURE [J].
YANKASKAS, JR ;
GATZY, JT ;
KNOWLES, MR ;
BOUCHER, RC .
LANCET, 1985, 1 (8435) :954-956
[34]   NONINVASIVE LIPOSOME-MEDIATED GENE DELIVERY CAN CORRECT THE ION-TRANSPORT DEFECT IN CYSTIC-FIBROSIS MUTANT MICE [J].
ALTON, EWFW ;
MIDDLETON, PG ;
CAPLEN, NJ ;
SMITH, SN ;
STEEL, DM ;
MUNKONGE, FM ;
JEFFERY, PK ;
GEDDES, DM ;
HART, SL ;
WILLIAMSON, R ;
FASOLD, KI ;
MILLER, AD ;
DICKINSON, P ;
STEVENSON, BJ ;
MCLACHLAN, G ;
DORIN, JR ;
PORTEOUS, DJ .
NATURE GENETICS, 1993, 5 (02) :135-142
[35]   EPITHELIAL MUCOUS GLYCOPROTEINS AND CYSTIC-FIBROSIS [J].
ROSE, MC .
HORMONE AND METABOLIC RESEARCH, 1988, 20 (10) :601-608
[36]   RESPIRATORY MUSCLE FUNCTION IN CYSTIC-FIBROSIS [J].
HOLZER, FJ ;
LANDAU, LI .
AUSTRALIAN PAEDIATRIC JOURNAL, 1981, 17 (02) :142-142
[37]   RESPIRATORY MUCINS AND INFECTION IN CYSTIC-FIBROSIS [J].
LAMBLIN, G ;
RAMPHAL, R .
PATHOLOGIE BIOLOGIE, 1991, 39 (06) :592-597
[38]   RESPIRATORY PHYSIOTHERAPY FOR CYSTIC-FIBROSIS - REPLY [J].
REISMAN, JJ ;
LEVISON, H .
JOURNAL OF PEDIATRICS, 1989, 115 (01) :168-168
[39]   RESPIRATORY MUSCLE SIZE IN CYSTIC-FIBROSIS [J].
HOPKINS, RL .
CHEST, 1984, 86 (02) :303-303
[40]   COEXISTENT RESPIRATORY ALLERGY AND CYSTIC-FIBROSIS [J].
RACHELEFSKY, GS ;
OSHER, A ;
DOOLEY, RE ;
ANK, B ;
STIEHM, ER .
AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1974, 128 (03) :355-359