PYODERMA-GANGRENOSUM, POLYCYTHEMIA-RUBRA-VERA, AND THE DEVELOPMENT OF LEUKEMIA

被引:41
作者
HO, KKL
OTRIDGE, BW
VANDENBERG, E
POWELL, FC
机构
[1] MATER MISERICORDIAE HOSP, REG CTR DERMATOL, ECCLES ST, DUBLIN 7, IRELAND
[2] MATER MISERICORDIAE HOSP, DEPT HEMATOL, DUBLIN, IRELAND
关键词
D O I
10.1016/0190-9622(92)70252-B
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
A patient with long-standing, well-controlled polycythemia rubra vera developed recurrent episodes of bullous pyoderma gangrenosum followed by the transformation of his hematologic disease into a rapidly progressive acute myeloid leukemia. This case, together with previously described patients, indicates that the appearance of bullous pyoderma gangrenosum in a patient with polycythemia rubra vera is often of ominous prognostic significance.
引用
收藏
页码:804 / 808
页数:5
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