PERIPHERAL-NERVE INVOLVEMENT IN CHILDREN WITH CHRONIC CHOLESTASIS AND VITAMIN-E-DEFICIENCY - A CLINICAL, ELECTROPHYSIOLOGICAL AND MORPHOLOGICAL-STUDY

被引:17
作者
LANDRIEU, P
SELVA, J
ALVAREZ, F
ROPERT, A
METRAL, S
机构
[1] UNIV PARIS 11,NEUROPATHOL EXPTL LAB,F-91405 ORSAY,FRANCE
[2] HOP BICETRE,HISTOEMBRYOL CYTOGENET LAB,F-94270 KREMLIN BICETRE,FRANCE
[3] HOP BICETRE,INSERM,U56,UNITE RECH HEPATOL INFANTILE,F-94270 KREMLIN BICETRE,FRANCE
[4] HOP BICETRE,NEUROPHYSIOL LAB,F-94270 KREMLIN BICETRE,FRANCE
关键词
D O I
10.1055/s-2008-1059536
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:194 / 201
页数:8
相关论文
共 14 条
[1]   HEPATIC DUCTULAR HYPOPLASIA ASSOCIATED WITH CHARACTERISTIC FACIES, VERTEBRAL MALFORMATIONS, RETARDED PHYSICAL, MENTAL AND SEXUAL DEVELOPMENT, AND CARDIAC MURMUR [J].
ALAGILLE, D ;
ODIEVRE, M ;
GAUTIER, M ;
DOMMERGUES, JP .
JOURNAL OF PEDIATRICS, 1975, 86 (01) :63-71
[2]  
ALVAREZ F, 1983, HEPATOLOGY, V3, P410
[3]  
ELIAS E, 1981, LANCET, V2, P1319
[4]   PROGRESSIVE NEUROMUSCULAR DISEASE IN CHILDREN WITH CHRONIC CHOLESTASIS AND VITAMIN-E-DEFICIENCY - DIAGNOSIS AND TREATMENT WITH ALPHA-TOCOPHEROL [J].
GUGGENHEIM, MA ;
RINGEL, SP ;
SILVERMAN, A ;
GRABERT, BE .
JOURNAL OF PEDIATRICS, 1982, 100 (01) :51-58
[5]  
LANDRIEU P, 1980, ARCH FR PEDIATR, V37, P445
[6]   LONG-TERM MANAGEMENT OF A-BETA-LIPOPROTEINEMIA - POSSIBLE ROLE FOR VITAMIN-E [J].
MULLER, DPR ;
LLOYD, JK ;
BIRD, AC .
ARCHIVES OF DISEASE IN CHILDHOOD, 1977, 52 (03) :209-214
[7]   PROGRESSIVE NEUROPATHOLOGIC LESIONS IN VITAMIN-E-DEFICIENT RHESUS-MONKEYS [J].
NELSON, JS ;
FITCH, CD ;
FISCHER, VW ;
BROUN, GO ;
CHOU, AC .
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1981, 40 (02) :166-186
[8]  
PENTSCHEW ANGEL, 1962, ACTA NEUROPATHOL, V1, P313
[9]   A PROGRESSIVE NEUROLOGIC SYNDROME IN CHILDREN WITH CHRONIC LIVER-DISEASE [J].
ROSENBLUM, JL ;
KEATING, JP ;
PRENSKY, AL ;
NELSON, JS .
NEW ENGLAND JOURNAL OF MEDICINE, 1981, 304 (09) :503-508
[10]   NEUROPATHOLOGY OF CHRONIC VITAMIN-E-DEFICIENCY IN FATAL FAMILIAL INTRA-HEPATIC CHOLESTASIS [J].
SAITO, K ;
YOKOYAMA, T ;
OKANIWA, M ;
KAMOSHITA, S .
ACTA NEUROPATHOLOGICA, 1982, 58 (03) :187-192