DECREASED LYMPHOCYTE COPROPORPHYRINOGEN-III OXIDASE ACTIVITY IN HEREDITARY COPROPORPHYRIA

被引:72
作者
GRANDCHAMP, B [1 ]
NORDMANN, Y [1 ]
机构
[1] HOP LOUIS MOURIER,FAC MED XAVIER BICHAT,DEPT BIOCHEM,F-92701 COLOMBES,FRANCE
关键词
D O I
10.1016/0006-291X(77)91630-8
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:1089 / 1095
页数:7
相关论文
共 18 条
[1]   ABNORMAL EXCRETION OF ISOMERS OF URINARY COPROPORPHYRIN BY PATIENTS WITH DUBIN-JOHNSON SYNDROME IN ISRAEL [J].
BENEZZER, J ;
RIMINGTON, C ;
SHANI, M ;
SELIGSOHN, U ;
SHEBA, C ;
SZEINBERG, A .
CLINICAL SCIENCE, 1971, 40 (01) :17-+
[2]   HEREDITARY COPROPORPHYRIA [J].
BERGER, H ;
GOLDBERG, A .
BRITISH MEDICAL JOURNAL, 1955, 2 (JUL9) :85-88
[3]   SIMULTANEOUS SEPARATION AND WASHING OF ERYTHROCYTES [J].
BLINCOE, C .
CLINICA CHIMICA ACTA, 1974, 57 (03) :297-300
[4]  
BOYUM A, 1968, SCAND J CLIN LAB S97, V21
[5]  
DOSS M, 1970, Z KLIN CHEM KLIN BIO, V8, P197
[6]  
ELDER GH, 1970, J CHROMATOG, V59, P234
[7]   APPLICATIONS OF HIGH-PRESSURE LIQUID-CHROMATOGRAPHY AND FIELD DESORPTION MASS-SPECTROMETRY IN STUDIES OF NATURAL PORPHYRINS AND CHLOROPHYLL DERIVATIVES [J].
EVANS, N ;
GAMES, DE ;
JACKSON, AH ;
MATLIN, SA .
JOURNAL OF CHROMATOGRAPHY, 1975, 115 (02) :325-333
[8]  
FALK JE, 1964, PORPHYRINS METALLOPO, P162
[9]   SPECTROPHOTOMETRIC DETERMINATION OF UROPORPHYRINOGEN I SYNTHETASE-ACTIVITY [J].
GRANDCHAMP, B ;
PHUNG, N ;
GRELIER, M ;
NORDMANN, Y .
CLINICA CHIMICA ACTA, 1976, 70 (01) :113-118
[10]   PORPHYRIN SYNTHESIS BY CULTURED LYMPHOCYTES [J].
JOSEPHSON, AS ;
SWERDLOW, F ;
LEVERE, RD ;
LOWENTHAL, I ;
GINSBERG, M .
BLOOD-THE JOURNAL OF HEMATOLOGY, 1972, 39 (04) :568-+