INCREASED VERY LONG-CHAIN FATTY-ACIDS IN PATIENTS ON A KETOGENIC DIET - A CAUSE OF DIAGNOSTIC CONFUSION

被引：27

作者：

THEDA, C

WOODY, RC

NAIDU, S

MOSER, AB

MOSER, HW

机构：

[1] UNIV MARYLAND, SCH MED, DEPT PEDIAT, BALTIMORE, MD 21201 USA

[2] JOHNS HOPKINS UNIV, SCH MED, DEPT PEDIAT, BALTIMORE, MD 21205 USA

[3] JOHNS HOPKINS UNIV, SCH MED, DEPT NEUROL, BALTIMORE, MD 21205 USA

来源：

JOURNAL OF PEDIATRICS | 1993年 / 122卷 / 05期

关键词：

D O I：

10.1016/S0022-3476(06)80013-2

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

We found on elevation of very long chain fatty acids in 13 of 22 plasma samples from patients on a ketogenic diet for the treatment of uncontrolled seizures. Because elevated values of very long chain fatty acids are a biochemical manifestation of peroxisomal dysfunction, this phenomenon might lead to diagnostic confusion. Thus the history and clinical status should be considered when plasma levels of very long chain fatty acids are interpreted.

引用

页码：724 / 726

页数：3

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