SYNTHESIS OF LYSOSOMAL ALPHA-MANNOSIDASE IN NORMAL AND MANNOSIDOSIS FIBROBLASTS

被引：27

作者：

POHLMANN, R ^{[1
]}

HASILIK, A ^{[1
]}

CHENG, S ^{[1
]}

PEMBLE, S ^{[1
]}

WINCHESTER, B ^{[1
]}

VONFIGURA, K ^{[1
]}

机构：

[1] UNIV LONDON QUEEN ELIZABETH COLL, DEPT BIOCHEM, LONDON W8 7AH, ENGLAND

来源：

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS | 1983年 / 115卷 / 03期

关键词：

D O I：

10.1016/S0006-291X(83)80046-1

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：1083 / 1089

页数：7

共 24 条

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[5] EVIDENCE THAT MUTANT ENZYME IN FIBROBLASTS OF A PATIENT WITH MANNOSIDOSIS DOES NOT CROSSREACT WITH ANTISERUM RAISED AGAINST NORMAL ACIDIC ALPHA-D-MANNOSIDASE [J].

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[8] SECRETION OF BETA-HEXOSAMINIDASE BY CULTURED HUMAN-SKIN FIBROBLASTS - KINETICS, EFFECT OF TEMPERATURE, CELL DENSITY, SERUM CONCENTRATION AND PH [J].

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