HYDROLYSIS OF GALACTOSYLSPHINGOSINE AND LACTOSYLSPHINGOSINE BY BETA-GALACTOSIDASES IN HUMAN-BRAIN AND CULTURED FIBROBLASTS

被引:12
作者
GODA, S [1 ]
KOBAYASHI, T [1 ]
GOTO, I [1 ]
机构
[1] KYUSHU UNIV 60,FAC MED,INST NEUROL,DEPT NEUROL,3-1-1 MAIDASHI,HIGASHI KU,FUKUOKA 812,JAPAN
关键词
D O I
10.1016/0005-2760(87)90103-2
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:259 / 265
页数:7
相关论文
共 18 条
[1]  
ETO Y, 1974, J BIOL CHEM, V249, P4955
[2]  
HANADA E, 1979, BIOCHIM BIOPHYS ACTA, V575, P410
[3]   PROGRESSIVE ACCUMULATION OF TOXIC METABOLITE IN A GENETIC LEUKODYSTROPHY [J].
IGISU, H ;
SUZUKI, K .
SCIENCE, 1984, 224 (4650) :753-755
[4]  
KOBAYASHI T, 1980, CLIN CHIM ACTA, V103, P343
[5]  
KOBAYASHI T, 1985, J BIOL CHEM, V260, P4982
[6]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[7]   GALACTOSYLSPHINGOSINE GALACTOSYL HYDROLASE IN RAT-BRAIN - PROBABLE IDENTITY WITH GALACTOSYLCERAMIDE GALACTOSYL HYDROLASE [J].
MIYATAKE, T ;
SUZUKI, K .
JOURNAL OF NEUROCHEMISTRY, 1974, 22 (02) :231-237
[8]  
MIYATAKE T, 1972, J BIOL CHEM, V247, P5398
[9]   GLOBOID CELL LEUKODYSTROPHY - ADDITIONAL DEFICIENCY OF PSYCHOSINE GALACTOSIDASE [J].
MIYATAKE, T ;
SUZUKI, K .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1972, 48 (03) :538-&
[10]  
PETERS SP, 1977, J BIOL CHEM, V252, P563