THE TREATABLE DEMENTIA OF SJOGRENS-SYNDROME

被引:68
作者
CASELLI, RJ
SCHEITHAUER, BW
BOWLES, CA
TRENERRY, MR
MEYER, FB
SMIGIELSKI, JS
RODRIGUEZ, M
机构
[1] MAYO CLIN & MAYO FDN,DEPT NEUROL,ROCHESTER,MN 55905
[2] MAYO CLIN & MAYO FDN,SURG PATHOL SECT,ROCHESTER,MN 55905
[3] MAYO CLIN & MAYO FDN,DIV RHEUMATOL & INTERNAL MED,ROCHESTER,MN 55905
[4] MAYO CLIN & MAYO FDN,DEPT NEUROL SURG,ROCHESTER,MN 55905
关键词
D O I
10.1002/ana.410300117
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Progressive dementia developed during a 15-month period in a 56-year-old woman with serologically and clinically documented primary Sjogren's syndrome. Findings from magnetic resonance imaging and angiography were normal, but a brain biopsy disclosed perivascular lymphocytic inflammation in leptomeningeal and parenchymal vessels. Treatment with high-dose corticosteroids produced rapid and nearly complete resolution of the dementia.
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收藏
页码:98 / 101
页数:4
相关论文
共 23 条
[1]   MAGNETIC-RESONANCE IMAGING OF CEREBRAL-LESIONS IN PATIENTS WITH THE SJOGREN SYNDROME [J].
ALEXANDER, EL ;
BEALL, SS ;
GORDON, B ;
SELNES, OA ;
YANNAKAKIS, GD ;
PATRONAS, N ;
PROVOST, TT ;
MCFARLAND, HF .
ANNALS OF INTERNAL MEDICINE, 1988, 108 (06) :815-823
[2]   ASEPTIC MENINGOENCEPHALITIS IN PRIMARY SJOGRENS SYNDROME [J].
ALEXANDER, EL ;
ALEXANDER, GE .
NEUROLOGY, 1983, 33 (05) :593-598
[3]   NEUROLOGIC COMPLICATIONS OF PRIMARY SJOGRENS SYNDROME [J].
ALEXANDER, EL ;
PROVOST, TT ;
STEVENS, MB ;
ALEXANDER, GE .
MEDICINE, 1982, 61 (04) :247-257
[4]  
ALEXANDER EL, 1986, SCAND J RHEUMATOL S, V61, P161
[5]   SJOGREN SYNDROME - CENTRAL NERVOUS-SYSTEM MANIFESTATIONS [J].
ALEXANDER, GE ;
PROVOST, TT ;
STEVENS, MB ;
ALEXANDER, EL .
NEUROLOGY, 1981, 31 (11) :1391-1396
[6]  
Benton A., 1983, MULTILINGUAL APHASIA, V3
[7]  
Benton AL, 1994, CONTRIBUTIONS NEUROP
[8]   GIANT-CELL (TEMPORAL) ARTERITIS - A TREATABLE CAUSE OF MULTIINFARCT DEMENTIA [J].
CASELLI, RJ .
NEUROLOGY, 1990, 40 (05) :753-755
[9]   POLYMORPHOUS MENINGITIS WITH ATYPICAL MONONUCLEAR-CELLS IN SJOGRENS SYNDROME [J].
DELAMONTE, SM ;
HUTCHINS, GM ;
GUPTA, PK .
ANNALS OF NEUROLOGY, 1983, 14 (04) :455-461
[10]   PROGRESSIVE APHASIA IN A PATIENT WITH PICKS DISEASE - A NEUROPSYCHOLOGICAL, RADIOLOGIC, AND ANATOMIC STUDY [J].
GRAFFRADFORD, NR ;
DAMASIO, AR ;
HYMAN, BT ;
HART, MN ;
TRANEL, D ;
DAMASIO, H ;
VANHOESEN, GW ;
REZAI, K .
NEUROLOGY, 1990, 40 (04) :620-626