THE TREATABLE DEMENTIA OF SJOGRENS-SYNDROME

被引:66
作者
CASELLI, RJ
SCHEITHAUER, BW
BOWLES, CA
TRENERRY, MR
MEYER, FB
SMIGIELSKI, JS
RODRIGUEZ, M
机构
[1] MAYO CLIN & MAYO FDN,DEPT NEUROL,ROCHESTER,MN 55905
[2] MAYO CLIN & MAYO FDN,SURG PATHOL SECT,ROCHESTER,MN 55905
[3] MAYO CLIN & MAYO FDN,DIV RHEUMATOL & INTERNAL MED,ROCHESTER,MN 55905
[4] MAYO CLIN & MAYO FDN,DEPT NEUROL SURG,ROCHESTER,MN 55905
关键词
D O I
10.1002/ana.410300117
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Progressive dementia developed during a 15-month period in a 56-year-old woman with serologically and clinically documented primary Sjogren's syndrome. Findings from magnetic resonance imaging and angiography were normal, but a brain biopsy disclosed perivascular lymphocytic inflammation in leptomeningeal and parenchymal vessels. Treatment with high-dose corticosteroids produced rapid and nearly complete resolution of the dementia.
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收藏
页码:98 / 101
页数:4
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