OSTEOGENESIS IMPERFECTA AND HYPERPLASTIC CALLUS FORMATION - LIGHT-MICROSCOPIC AND ELECTRON-MICROSCOPIC FINDINGS

被引:8
|
作者
STOSS, H
PONTZ, B
VETTER, U
KARBOWSKI, A
BRENNER, R
SPRANGER, J
机构
[1] UNIV MUNICH,DEPT PAEDIAT,W-8000 MUNICH 2,GERMANY
[2] UNIV ULM,DEPT PAEDIAT,W-7900 ULM,GERMANY
[3] UNIV MUNSTER,DEPT ORTHOPAED,W-4400 MUNSTER,GERMANY
[4] UNIV MUNSTER,DEPT PAEDIAT,W-4400 MUNSTER,GERMANY
来源
AMERICAN JOURNAL OF MEDICAL GENETICS | 1993年 / 45卷 / 02期
关键词
OSTEOGENESIS IMPERFECTA; HYPERPLASTIC CALLUS; DESMALCHONDRAL OSTEONEOGENESIS; ATYPICAL COLLAGEN FIBRILS;
D O I
10.1002/ajmg.1320450222
中图分类号
Q3 [遗传学];
学科分类号
071007 ; 090102 ;
摘要
In rare cases of osteogenesis imperfecta, an ''overshoot'' growth of new bone may occur, which, clinically gives the impression of a tumour. This condition is known as hyperplastic callus formation. Morphology showed an excessive mixed desmal-chondral osteoneogenesis. Atypical collagen fibrils in non-callus tissue represent an indicator for this callus formation in individual patients.
引用
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页码:260 / 260
页数:1
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