MULTIPLE NEUTRAL MALTASE ACTIVITIES IN NORMAL AND ACID MALTASE-DEFICIENT HUMAN-MUSCLE

被引:7
|
作者
SHANSKE, S
BRESOLIN, N
DIMAURO, S
机构
关键词
D O I
10.1016/0014-4886(84)90204-8
中图分类号
Q189 [神经科学];
学科分类号
071006 ;
摘要
引用
收藏
页码:565 / 578
页数:14
相关论文
共 50 条
  • [1] IMMUNOCYTOCHEMICAL ANALYSIS OF NORMAL AND ACID MALTASE-DEFICIENT MUSCLE CULTURES
    MIRANDA, AF
    SHANSKE, S
    HAYS, AP
    DIMAURO, S
    ARCHIVES OF NEUROLOGY, 1985, 42 (04) : 371 - 373
  • [2] ISOELECTRIC-FOCUSING STUDIES OF ACID AND NEUTRAL MALTASE IN HUMAN-MUSCLE
    SHANSKE, S
    MIRANDA, AF
    DIMAURO, S
    JOURNAL OF CELL BIOLOGY, 1981, 91 (02): : A357 - A357
  • [3] REAPPEARANCE OF EMBRYONIC NEUTRAL ALPHA-GLUCOSIDASE ISOENZYME IN ACID MALTASE-DEFICIENT MUSCLE OF JAPANESE QUAIL
    USUKI, F
    ISHIURA, S
    HIGUCHI, I
    SUGITA, H
    EXPERIMENTAL NEUROLOGY, 1988, 100 (02) : 394 - 402
  • [4] ALPHA-GLUCOSIDASE ISOENZYMES IN NORMAL AND ACID MALTASE-DEFICIENT HUMAN SKELETAL-MUSCLES
    USUKI, F
    ISHIURA, S
    NONAKA, I
    SUGITA, H
    MUSCLE & NERVE, 1988, 11 (04) : 365 - 371
  • [5] SUBCELLULAR-DISTRIBUTION OF ACID AND NEUTRAL ALPHA-GLUCOSIDASES IN NORMAL, ACID MALTASE DEFICIENT, AND MYOPHOSPHORYLASE DEFICIENT HUMAN SKELETAL-MUSCLE
    ANGELINI, C
    ENGEL, AG
    ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1973, 156 (01) : 350 - 355
  • [6] Clinical and metabolic correction of Pompe disease by enzyme therapy in acid maltase-deficient quail
    Kikuchi, T
    Yang, HW
    Pennybacker, M
    Ichihara, N
    Mizutani, M
    Van Hove, JLK
    Chen, YT
    JOURNAL OF CLINICAL INVESTIGATION, 1998, 101 (04): : 827 - 833
  • [7] ELECTROPHORETIC RESEARCH ON ALPHA GLUCOSIDASE (ACID MALTASE) IN NORMAL AND DEFICIENT SUBJECTS
    DREYFUS, JC
    ARCHIVES FRANCAISES DE PEDIATRIE, 1973, 30 (04): : 457 - 457
  • [8] MUSCLE ULTRASTRUCTURE IN ACID MALTASE DEFICIENCY
    GRIFFIN, JL
    ARMBRUSTMACHER, VW
    JOURNAL OF CELL BIOLOGY, 1977, 75 (02): : A328 - A328
  • [9] HUMAN ACID MALTASE-DEFICIENT MYOGENIC CELL-TRANSFORMATION WITH ORIGIN-DEFECTIVE SV40 - CHARACTERIZATION OF A CLONED LINE
    USUKI, F
    HIGUCHI, I
    SOEJIMA, Y
    HATTORI, M
    MARUYAMA, I
    OSAME, M
    MUSCLE & NERVE, 1991, 14 (03) : 245 - 252
  • [10] IMMUNOCYTOCHEMICAL STUDIES OF ACID MALTASE IN HUMAN FIBROBLAST AND MUSCLE CULTURES
    HAYS, AP
    MIRANDA, AF
    MEHLER, M
    DIMAURO, S
    IN VITRO-JOURNAL OF THE TISSUE CULTURE ASSOCIATION, 1979, 15 (03): : 204 - 204