INTESTINAL LYMPHANGIECTASIA IN A PATIENT WITH AUTOIMMUNE POLYGLANDULAR DISEASE TYPE-I AND STEATORRHEA

被引：21

作者：

BEREKET, A

LOWENHEIM, M

BLETHEN, SL

KANE, P

WILSON, TA

机构：

[1] SUNY STONY BROOK, DEPT PEDIAT, STONY BROOK, NY 11794 USA

[2] SUNY STONY BROOK, DEPT PATHOL, STONY BROOK, NY 11794 USA

来源：

JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM | 1995年 / 80卷 / 03期

关键词：

D O I：

10.1210/jc.80.3.933

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Steatorrhea is seen in 18-24% of patients with autoimmune polyglandular disease (APD) type 1. The etiology and pathophysiology of the steatorrhea in this disease are unknown. We present a patient with APD type 1 and steatorrhea in whom biopsies revealed intestinal lymphangiectasia. This association has not been previously described. Intestinal lymphangiectasia may explain the steatorrhea in some patients with APD type 1. As blind intestinal biopsies may miss areas of intestinal lymphangiectasia, endoscopically directed intestinal biopsies should be included in the evaluation of steatorrhea in APD type 1.

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页码：933 / 935

页数：3

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