INCREASED INTRACRANIAL-PRESSURE IN ALEXANDER DISEASE - A RARE PRESENTATION OF WHITE-MATTER DISEASE

被引：17
作者：
GARCIA, L
GASCON, G
OZAND, P
YAISH, H
机构：
[1] KING FAHD NATL GUARD HOSP,RIYADH,SAUDI ARABIA
[2] KING FAISAL SPECIALIST HOSP & RES CTR,RIYADH 11211,SAUDI ARABIA
来源：
JOURNAL OF CHILD NEUROLOGY | 1992年 / 7卷 / 02期
关键词：
D O I：
10.1177/088307389200700206
中图分类号：
R74 [神经病学与精神病学];
学科分类号：
摘要：
A patient with biopsy-proven Alexander disease presented with progressive head enlargement and clinical evidence of increased intracranial pressure. Lumbar puncture under sedation confirmed increased intracranial pressure with otherwise normal cerebrospinal fluid values. The association of megalencephaly, increased intracranial pressure and neuroimaging evidence of leukoencephalopathy should alert pediatric neurologists to the possibility of Alexander disease.
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页码：168 / 171
页数：4
相关论文
共 8 条
[1]   PROGRESSIVE FIBRINOID DEGENERATION OF FIBRILLARY ASTROCYTES ASSOCIATED WITH MENTAL RETARDATION IN A HYDROCEPHALIC INFANT [J].
ALEXANDER, WS .
BRAIN, 1949, 72 (03) :373-&
[2]   ALEXANDERS DISEASE - A DISEASE OF ASTROCYTES [J].
BORRETT, D ;
BECKER, LE .
BRAIN, 1985, 108 (JUN) :367-385
[3]   ALEXANDERS DISEASE - CASE-REPORT INCLUDING HISTO-PATHOLOGICAL AND ELECTRON-MICROSCOPIC FEATURES [J].
COLE, G ;
DEVILLIERS, F ;
PROCTOR, NSF ;
FREIMAN, I ;
BILL, P .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1979, 42 (07) :619-624
[4]   COMPUTED-TOMOGRAPHY IN ALEXANDERS DISEASE [J].
FARRELL, K ;
CHUANG, S ;
BECKER, LE .
ANNALS OF NEUROLOGY, 1984, 15 (06) :605-607
[5]   ASPARTOACYLASE DEFICIENCY AND N-ACETYLASPARTIC ACIDURIA IN PATIENTS WITH CANAVAN DISEASE [J].
MATALON, R ;
MICHALS, K ;
SEBESTA, D ;
DEANCHING, M ;
GASHKOFF, P ;
CASANOVA, J .
AMERICAN JOURNAL OF MEDICAL GENETICS, 1988, 29 (02) :463-471
[6]   ASPARTOACYLASE DEFICIENCY AND CANAVAN DISEASE IN SAUDI-ARABIA [J].
OZAND, PT ;
GASCON, GG ;
DHALLA, M .
AMERICAN JOURNAL OF MEDICAL GENETICS, 1990, 35 (02) :266-268
[7]   ALEXANDERS DISEASE - REPORT AND REAPPRAISAL [J].
RUSSO, LS ;
ARON, A ;
ANDERSON, PJ .
NEUROLOGY, 1976, 26 (07) :607-614
[8]   ALEXANDERS DISEASE - FURTHER LIGHT-MICROSCOPIC, AND ELECTRON-MICROSCOPIC OBSERVATIONS [J].
TOWFIGHI, J ;
YOUNG, R ;
SASSANI, J ;
RAMER, J ;
HOROUPIAN, DS .
ACTA NEUROPATHOLOGICA, 1983, 61 (01) :36-42
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