BLUE RUBBER-BLEB NEVUS SYNDROME - REPORT OF A CASE WITH CONSUMPTION COAGULOPATHY COMPLICATED BY MANIFEST THROMBOSIS

被引:33
作者
HOFHUIS, WJD
ORANJE, AP
BOUQUET, J
SINAASAPPEL, M
机构
[1] ERASMUS UNIV,DEPT DERMATOL & VENEREOL,DIV PAEDIAT DERMATOL,3038 GE ROTTERDAM,NETHERLANDS
[2] UNIV HOSP ROTTERDAM,SOPHIA CHILDRENS HOSP,3038 GE ROTTERDAM,NETHERLANDS
[3] ERASMUS UNIV,DEPT PAEDIAT,DIV GASTROENTEROL,3038 GE ROTTERDAM,NETHERLANDS
关键词
Aspirin; Blue rubber-bleb naevus; Consumption coagulopathy; Thrombosis;
D O I
10.1007/BF01957684
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Blue rubber-bleb naevus (BRBN) syndrome is a rare disorder characterized by subcutaneous and gastrointestinal haemangiomas. The latter may lead to bleeding complications. A case is reported in which a process of chronic intravascular coagulation resulted in serious thrombotic complications. In the presence of a chronic consumption coagulopathy, it remains uncertain whether antiplatelet drugs are of prophylactic antithrombotic value. © 1990 Springer-Verlag.
引用
收藏
页码:526 / 528
页数:3
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